CONGENITAL DEFICIENCY OF 2 POLYPEPTIDE SUBUNITS OF THE IRON PROTEIN-FRAGMENT OF MITOCHONDRIAL COMPLEX-I

被引：41

作者：

MOREADITH, RW

CLEETER, MWJ

RAGAN, CI

BATSHAW, ML

LEHNINGER, AL

机构：

[1] JOHNS HOPKINS UNIV,SCH MED,KENNEDY INST,707 N BROADWAY,BALTIMORE,MD 21205

[2] JOHNS HOPKINS UNIV,SCH MED,DEPT PEDIAT,BALTIMORE,MD 21205

[3] JOHNS HOPKINS UNIV,SCH MED,DEPT BIOL CHEM,BALTIMORE,MD 21205

[4] DUKE UNIV,MED CTR,DEPT INTERNAL MED,DURHAM,NC 27710

[5] UNIV SOUTHAMPTON,DEPT BIOCHEM,SOUTHAMPTON SO9 3TU,HANTS,ENGLAND

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1987年 / 79卷 / 02期

关键词：

D O I：

10.1172/JCI112834

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：463 / 467

页数：5

共 22 条

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[10] DEFICIENCY OF THE IRON-SULFUR CLUSTERS OF MITOCHONDRIAL REDUCED NICOTINAMIDE-ADENINE DINUCLEOTIDE-UBIQUINONE OXIDOREDUCTASE (COMPLEX-I) IN AN INFANT WITH CONGENITAL LACTIC-ACIDOSIS [J].

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