SCLERODERMA-LIKE SKIN-LESIONS IN 2 PATIENTS WITH PHENYLKETONURIA

被引:4
作者
COSKUN, T [1 ]
OZALP, I [1 ]
KALE, G [1 ]
GOGUS, S [1 ]
机构
[1] HACETTEPE UNIV,INST CHILD HLTH,DIV PATHOL,ANKARA,TURKEY
关键词
Phenylketonuria; Scleroderma;
D O I
10.1007/BF02072050
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Two patients with phenylketonuria and scleroderma-like skin lesions are presented. Since scleroderma is a rare collagen disease of childhood, the occurrence of these two disorders in the same patient does not seem to be coincidental but raises the possibility of a causal relationship. Improvement in the skin lesions of the patients after the commencement of a low-phenylalanine diet supports this hypothesis. © 1990 Springer-Verlag.
引用
收藏
页码:109 / 110
页数:2
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