DEFICIENCY OF ELECTRON-TRANSFER FLAVOPROTEIN OR ELECTRON-TRANSFER FLAVOPROTEIN - UBIQUINONE OXIDOREDUCTASE IN GLUTARIC ACIDEMIA TYPE-II FIBROBLASTS

被引:142
作者
FRERMAN, FE [1 ]
GOODMAN, SI [1 ]
机构
[1] UNIV COLORADO,HLTH SCI CTR,DEPT PEDIAT,DENVER,CO 80262
关键词
D O I
10.1073/pnas.82.13.4517
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:4517 / 4520
页数:4
相关论文
共 34 条
  • [1] BECKMANN JD, 1983, J BIOL CHEM, V258, P7563
  • [2] BECKMANN JD, 1984, THESIS MED COLLEGE W
  • [3] BECKMANN JD, 1983, FED P FED AM SOC EXP, V42, P1761
  • [4] BURNETTE WN, 1981, ANAL BIOCHEM, V112, P195, DOI 10.1016/0003-2697(81)90281-5
  • [5] COUDE FX, 1981, HUM GENET, V59, P263
  • [6] CRANE FL, 1956, J BIOL CHEM, V218, P717
  • [7] PATTERN OF IRON-SULFUR CENTERS IN BROWN ADIPOSE-TISSUE MITOCHONDRIA - PREPONDERANCE OF ETF DEHYDROGENASE AND INVARIANCE WITH THERMOGENIC STATE
    FLATMARK, T
    RUZICKA, FJ
    BEINERT, H
    [J]. FEBS LETTERS, 1976, 63 (01) : 51 - 55
  • [8] FRERMAN FE, 1983, J BIOL CHEM, V258, P7087
  • [9] GLUTARIC ACIDEMIA TYPE-II (MULTIPLE ACYL-COA DEHYDROGENATION DEFICIENCY)
    GOODMAN, SI
    FRERMAN, FE
    [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1984, 7 : 33 - 37
  • [10] GLUTARIC ACIDEMIA TYPE-II - A FORM WITH DELETERIOUS INTRAUTERINE EFFECTS
    GOODMAN, SI
    REALE, M
    BERLOW, S
    [J]. JOURNAL OF PEDIATRICS, 1983, 102 (03) : 411 - 413