STRUMPELL FAMILIAL SPASTIC PARAPLEGIA - AN ELECTROPHYSIOLOGICAL DEMONSTRATION OF SELECTIVE CENTRAL DISTAL AXONOPATHY

被引:12
作者
UNCINI, A [1 ]
TREVISO, M [1 ]
BASCIANI, M [1 ]
GAMBI, D [1 ]
机构
[1] UNIV CHIETI, INST NEUROL SCI, CLIN NEUROPHYSIOL LAB, CHIETI, ITALY
来源
ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY | 1987年 / 66卷 / 02期
关键词
D O I
10.1016/0013-4694(87)90182-9
中图分类号
R318 [生物医学工程];
学科分类号
0831 ;
摘要
Three patients with autosomal dominant Strumpell''s familial spastic paraplegia (SFSP) were evaluated by means of somatosensory evoked potentials (SEPs) from upper and lower limb and determination of sural nerve conduction velocity. Findings of normal sural nerve conduction but reduced amplitude and poor definition of SEPs with normal latencies on peroneal nerve stimulation support a pattern of central nervous system degeneration characterized by a selective involvement of centrally directed axons within the gracile fasciculi.
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收藏
页码:132 / 136
页数:5
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