INVIVO AND INVITRO STUDIES ON FORMATION OF BILE-ACIDS IN PATIENTS WITH ZELLWEGER SYNDROME - EVIDENCE THAT PEROXISOMES ARE OF IMPORTANCE IN THE NORMAL BIOSYNTHESIS OF BOTH CHOLIC AND CHENODEOXYCHOLIC ACID

被引：61

作者：

KASE, BF

PEDERSEN, JI

STRANDVIK, B

BJORKHEM, I

机构：

[1] HUDDINGE UNIV HOSP,KAROLINSKA INST,DEPT CLIN CHEM,S-14186 HUDDINGE,SWEDEN

[2] HUDDINGE UNIV HOSP,KAROLINSKA INST,DEPT PEDIAT,S-14186 HUDDINGE,SWEDEN

[3] HUDDINGE UNIV HOSP,KAROLINSKA INST,RES CTR,S-14186 HUDDINGE,SWEDEN

[4] UNIV OSLO,SCH MED,INST NUTR RES,OSLO 3,NORWAY

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1985年 / 76卷 / 06期

关键词：

D O I：

10.1172/JCI112252

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：2393 / 2402

页数：10

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