IMPAIRED SECRETION OF TYPE-III PROCOLLAGEN IN EHLERS-DANLOS SYNDROME TYPE-IV FIBROBLASTS - CORRECTION OF THE DEFECT BY INCUBATION AT REDUCED TEMPERATURE AND DEMONSTRATION OF SUBTLE ALTERATIONS IN THE TRIPLE-HELICAL REGION OF THE MOLECULE

被引：36

作者：

SUPERTIFURGA, A

STEINMANN, B

机构：

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1988年 / 150卷 / 01期

关键词：

D O I：

10.1016/0006-291X(88)90497-4

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：140 / 147

页数：8

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