SUBTOTAL SPLENECTOMY IN GAUCHERS-DISEASE - TOWARDS A DEFINITION OF CRITICAL SPLENIC MASS

被引:5
作者
ZER, M [1 ]
FREUD, E [1 ]
机构
[1] TEL AVIV UNIV, SACKLER SCH MED, TEL AVIV, ISRAEL
关键词
D O I
10.1002/bjs.1800790806
中图分类号
R61 [外科手术学];
学科分类号
摘要
Partial splenectomy is currently the favoured surgical approach for Gaucher's disease. Preservation of splenic tissue is indicated to prevent susceptibility to overwhelming postsplenectomy sepsis, to delay the massive deposition of glucocerebroside in the liver and bones, and to relieve symptoms of hypersplenism. Controversial issues and technical problems related to partial splenectomy for Gaucher's disease are discussed and a definition of critical splenic mass considered.
引用
收藏
页码:742 / 744
页数:3
相关论文
共 35 条
  • [1] BARMAOR JA, 1985, PEDIATRICS, V76, P398
  • [2] BARMAOR JA, 1989, PEDIATR SURG INT, V4, P205
  • [3] COHEN IJ, 1992, IN PRESS AM J SURG
  • [4] DEFECTIVE PHAGOCYTOSIS DUE TO TUFTSIN DEFICIENCY IN SPLENECTOMIZED SUBJECTS
    CONSTANT.A
    NAJJAR, VA
    WISH, JB
    NECHELES, TH
    STOLBACH, LL
    [J]. AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1973, 125 (05): : 663 - 665
  • [5] COONEY DR, 1979, SURGERY, V86, P561
  • [6] Coppoletta JM, 1933, AM J PATHOL, V9, P55
  • [7] DREW PA, 1984, J IMMUNOL, V132, P191
  • [8] GAUCHER DISEASE - FATE OF THE SPLENIC REMNANT AFTER PARTIAL SPLENECTOMY - A CASE OF RAPID ENLARGEMENT
    FLESHNER, PR
    ASTION, DJ
    LUDMAN, MD
    AUFSES, AH
    GRABOWSKI, GA
    DOLGIN, SE
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1989, 24 (06) : 610 - 612
  • [9] 95 PERCENT SPLENECTOMY FOR MASSIVE SPLENOMEGALY - A NEW SURGICAL APPROACH
    FONKALSRUD, EW
    PHILIPPART, M
    FEIG, S
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1990, 25 (02) : 267 - 269
  • [10] GOVRINYEHUDAIN J, 1980, ISRAEL J MED SCI, V16, P665