GLUTATHIONURIA - INBORN ERROR OF METABOLISM DUE TO TISSUE DEFICIENCY OF GAMMA-GLUTAMYL TRANSPEPTIDASE

被引:127
作者
SCHULMAN, JD
GOODMAN, SI
MACE, JW
PATRICK, AD
TIETZE, F
BUTLER, EJ
机构
[1] NIH,BETHESDA,MD 20014
[2] UNIV COLORADO,MED CTR,DEPT PEDIAT,DENVER,CO
[3] LOMA LINDA UNIV,MED CTR,DEPT PEDIAT,LOMA LINDA,CA
[4] UNIV LONDON,INST CHILD HLTH,LONDON,ENGLAND
关键词
D O I
10.1016/S0006-291X(75)80062-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:68 / 74
页数:7
相关论文
共 19 条
[1]   HISTOCHEMICAL DEMONSTRATION OF GAMMA-GLUTAMYL TRANSPEPTIDASE [J].
ALBERT, Z ;
ORLOWSKI, M ;
SZEWCZUK, A .
NATURE, 1961, 191 (479) :767-&
[2]  
BINKLEY F, 1961, J BIOL CHEM, V236, P1075
[3]  
BINKLEY F, 1974, SCIENCE, V184, P586, DOI 10.1126/science.184.4136.586
[4]   METABOLISM OF GLUTATHIONE [J].
BINKLEY, F .
NATURE, 1951, 167 (4257) :888-889
[5]   MEMBRANE-BOUND GAMMA-GLUTAMYL TRANSPEPTIDASE - EVIDENCE THAT IT IS A COMPONENT OF AMINO-ACID SITE OF CERTAIN NEUTRAL AMINO-ACID TRANSPORT-SYSTEMS [J].
BODNARYK, RP .
CANADIAN JOURNAL OF BIOCHEMISTRY, 1972, 50 (05) :524-&
[6]  
COPPOLA PT, IN PRESS
[7]  
DICKINSON JC, 1965, PEDIATRICS, V36, P2
[8]  
GOODMAN SI, 1971, LANCET, V1, P234
[9]   SYNTHESIS OF PEPTIDES IN ENZYMIC REACTIONS INVOLVING GLUTATHIONE [J].
HANES, CS ;
HIRD, FJR ;
ISHERWOOD, FA .
NATURE, 1950, 166 (4216) :288-292
[10]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265