MOLECULAR ANALYSIS OF PEROXISOMAL BETA-OXIDATION ENZYMES IN INFANTS WITH PEROXISOMAL DISORDERS INDICATES HETEROGENEITY OF THE PRIMARY DEFECT

被引:12
作者
GUERROUI, S
AUBOURG, P
CHEN, WW
HASHIMOTO, T
SCOTTO, J
机构
[1] HOP ST VINCENT PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
[2] JOHNS HOPKINS UNIV,SCH MED,KENNEDY INST,BALTIMORE,MD 21205
[3] JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
[4] SHINSHU UNIV,SCH MED,DEPT BIOCHEM,MATSUMOTO,NAGANO 390,JAPAN
关键词
D O I
10.1016/0006-291X(89)91587-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:242 / 251
页数:10
相关论文
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