DEFICIENCY OF PYRUVATE-DEHYDROGENASE COMPLEX (PDHC) IN LEIGHS DISEASE FIBROBLASTS - AN ABNORMALITY IN LIPOAMIDE DEHYDROGENASE AFFECTING PDHC ACTIVATION

被引：16

作者：

HINMAN, LM

SHEU, KFR

BAKER, AC

KIM, YT

BLASS, JP

机构：

[1] CORNELL UNIV,MED CTR,COLL MED,DEPT MED,NEW YORK,NY 10021

[2] CORNELL UNIV,COLL MED,BURKE REHABIL CTR,DEPT NEUROL,WHITE PLAINS,NY 10605

来源：

NEUROLOGY | 1989年 / 39卷 / 01期

关键词：

D O I：

10.1212/WNL.39.1.70

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：70 / 75

页数：6

共 42 条

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