LEIGHS DISEASE - SIGNIFICANCE OF BIOCHEMICAL CHANGES IN BRAIN

被引:6
作者
MURPHY, JV
CRAIG, L
机构
[1] UNIV PITTSBURGH,SCH MED,DEPT PEDIAT,PITTSBURGH,PA 15213
[2] UNIV PITTSBURGH,SCH MED,DEPT NEUROL,PITTSBURGH,PA 15213
[3] CHILDRENS HOSP,PITTSBURGH,PA 15213
关键词
D O I
10.1136/jnnp.38.11.1100
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1100 / 1103
页数:4
相关论文
共 13 条
[1]   THIAMINE TRIPHOSPHATE DEFICIENCY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].
COOPER, JR ;
ITOKAWA, Y ;
PINCUS, JH .
SCIENCE, 1969, 164 (3875) :74-&
[2]   ROLE OF THIAMINE TRIPHOSPHATE IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].
COOPER, JR ;
PINCUS, JH .
JOURNAL OF AGRICULTURAL AND FOOD CHEMISTRY, 1972, 20 (03) :490-&
[3]   BIOCHEMICAL STUDIES AND THERAPY IN SUBACUTE NECROTIZING ENCEPBALOMYELOPATHY (LEIGHS SYNDROME) [J].
GROVER, WD ;
PATEL, MS ;
AUERBACH, VH .
JOURNAL OF PEDIATRICS, 1972, 81 (01) :39-+
[4]   LEIGHS ENCEPHALOMYELOPATHY - AN INBORN ERROR OF GLUCONEOGENESIS [J].
HOMMES, FA ;
POLMAN, HA ;
REERINK, JD .
ARCHIVES OF DISEASE IN CHILDHOOD, 1968, 43 (230) :423-&
[5]  
ITOKAWA Y., 1970, Methods in Enzymology, V18A, P91, DOI 10.1016/0076-6879(71)18284-5
[6]   ION MOVEMENTS AND THIAMINE .2. RELEASE OF VITAMIN FROM MEMBRANE FRAGMENTS [J].
ITOKAWA, Y ;
COOPER, JR .
BIOCHIMICA ET BIOPHYSICA ACTA, 1970, 196 (02) :274-&
[7]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]   SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY - REVIEW AND A STUDY OF 2 FAMILIES [J].
MONTPETIT, VJ ;
ANDERMANN, F ;
CARPENTER, S ;
FAWCETT, JS ;
ZBOROWSK.D ;
GIBERSON, HR .
BRAIN, 1971, 94 :1-+
[9]  
MURPHY JV, 1974, DEV MED CHILD NEUROL, V16, P362
[10]   LEIGH DISEASE [J].
MURPHY, JV ;
CRAIG, LJ ;
GLEW, RH .
ARCHIVES OF NEUROLOGY, 1974, 31 (04) :220-227