EXCESSIVE EXCRETION OF BETA-ALANINE AND OF 3-HYDROXYPROPIONIC, R-3-AMINOISOBUTYRIC AND S-3-AMINOISOBUTYRIC, R-3-HYDROXYISOBUTYRIC AND S-3-HYDROXYISOBUTYRIC AND S-2-(HYDROXYMETHYL)BUTYRIC ACIDS PROBABLY DUE TO A DEFECT IN THE METABOLISM OF THE CORRESPONDING MALONIC SEMIALDEHYDES

被引：50

作者：

POLLITT, RJ

GREEN, A

SMITH, R

机构：

[1] CHILDRENS HOSP,DEPT CLIN CHEM,BIRMINGHAM B16 8ET,W MIDLANDS,ENGLAND

[2] ROYAL INFIRM,DEPT BIOCHEM,BRADFORD BD9 6RJ,ENGLAND

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1985年 / 8卷 / 02期

关键词：

D O I：

10.1007/BF01801669

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：75 / 79

页数：5

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