PATHOLOGICAL FINDINGS AT THE SITE OF CONDUCTION BLOCK IN MULTIFOCAL MOTOR NEUROPATHY

被引:183
作者
KAJI, R
OKA, N
TSUJI, T
MEZAKI, T
NISHIO, T
AKIGUCHI, I
KIMURA, J
机构
[1] Department of Neurology, Kyoto University Hospital, Kyoto, Sakyoku
关键词
D O I
10.1002/ana.410330204
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report on 2 patients with multifocal motor neuropathy with focal conduction block involving motor but not sensory fibers at the site of nerve swelling. A nerve biopsy specimen from adjacent to the enlargement in 1 patient showed a perivascular area containing scattered demyelinated axons surrounded by small onion bulbs. The observed pathological findings are consistent with the conduction block considered characteristic of this neuropathy, although the underlying immunological mechanisms for selectivity and persistence remain undetermined.
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页码:152 / 158
页数:7
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