REGIONAL MITOCHONDRIAL RESPIRATORY ACTIVITY IN HUNTINGTONS-DISEASE BRAIN

被引:224
作者
BRENNAN, WA
BIRD, ED
APRILLE, JR
机构
[1] MASSACHUSETTS GEN HOSP,DEPT NEUROL,BOSTON,MA 02114
[2] HARVARD UNIV,MCLEAN HOSP,SCH MED,RALPH LOWELL LAB,BELMONT,MA 02178
[3] TUFTS UNIV,DEPT BIOL,MEDFORD,MA 02155
关键词
D O I
10.1111/j.1471-4159.1985.tb07192.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1948 / 1950
页数:3
相关论文
共 30 条
[1]   POSTNATAL-DEVELOPMENT OF RAT-LIVER MITOCHONDRIA - STATE-3 RESPIRATION, ADENINE-NUCLEOTIDE TRANSLOCASE ACTIVITY, AND THE NET ACCUMULATION OF ADENINE-NUCLEOTIDES [J].
APRILLE, JR ;
ASIMAKIS, GK .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1980, 201 (02) :564-575
[2]   SEX RELATED FACTOR IN INHERITANCE OF HUNTINGTONS-CHOREA [J].
BIRD, ED ;
CARO, AJ ;
PILLING, JB .
ANNALS OF HUMAN GENETICS, 1974, 37 (JAN) :255-260
[3]  
BOEHNKE M, 1983, AM J HUM GENET, V35, P845
[4]   MITOCHONDRIAL CYTOCHROME DEFICIENCY PRESENTING AS A MYOPATHY WITH HYPOTONIA, EXTERNAL OPHTHALMOPLEGIA, AND LACTIC-ACIDOSIS IN AN INFANT AND AS FATAL HEPATOPATHY IN A 2ND COUSIN [J].
BOUSTANY, RN ;
APRILLE, JR ;
HALPERIN, J ;
LEVY, H ;
DELONG, GR .
ANNALS OF NEUROLOGY, 1983, 14 (04) :462-470
[5]   FAMILIAL CORRELATIONS FOR AGE AT ONSET AND AGE AT DEATH IN HUNTINGTONS DISEASE [J].
BRACKENRIDGE, CJ .
JOURNAL OF MEDICAL GENETICS, 1972, 9 (01) :23-+
[6]  
BRUYN GW, 1979, ADV NEUROL, V23, P83
[7]  
FORNO LS, 1973, ADV NEUROL, V1, P453
[8]   MATERNAL INHERITANCE OF HUMAN MITOCHONDRIAL-DNA [J].
GILES, RE ;
BLANC, H ;
CANN, HM ;
WALLACE, DC .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (11) :6715-6719
[9]   A POLYMORPHIC DNA MARKER GENETICALLY LINKED TO HUNTINGTONS-DISEASE [J].
GUSELLA, JF ;
WEXLER, NS ;
CONNEALLY, PM ;
NAYLOR, SL ;
ANDERSON, MA ;
TANZI, RE ;
WATKINS, PC ;
OTTINA, K ;
WALLACE, MR ;
SAKAGUCHI, AY ;
YOUNG, AB ;
SHOULSON, I ;
BONILLA, E ;
MARTIN, JB .
NATURE, 1983, 306 (5940) :234-238
[10]   ISOLATION, SUBUNIT COMPOSITION, AND SITE OF SYNTHESIS OF HUMAN CYTOCHROME C-OXIDASE [J].
HARE, JF ;
CHING, E ;
ATTARDI, G .
BIOCHEMISTRY, 1980, 19 (10) :2023-2030