SPASTIC PARAPARESIS ASSOCIATED WITH PORTAL-SYSTEMIC VENOUS SHUNTING DUE TO CONGENITAL HEPATIC-FIBROSIS

被引:34
作者
DEMIRCI, M [1 ]
TAN, E [1 ]
ELIBOL, B [1 ]
GEDIKOGLU, G [1 ]
SARIBAS, O [1 ]
机构
[1] HACETTEPE UNIV,FAC MED,DEPT PATHOL,ANKARA,TURKEY
关键词
D O I
10.1212/WNL.42.5.983
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a case of progressive spastic paraparesis in a 45-year-old man with total portal-systemic shunting, which developed spontaneously due to congenital hepatic fibrosis. Cellular functions of the liver, except for an elevated blood ammonia level, were within normal limits, as is usual in congenital hepatic fibrosis. This case shows that spastic paraparesis following portal-systemic shunting may occur without liver failure.
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页码:983 / 985
页数:3
相关论文
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