POLYARTHRITIS RESEMBLING JUVENILE RHEUMATOID-ARTHRITIS IN A GIRL WITH CHRONIC GRANULOMATOUS-DISEASE

被引:43
作者
LEE, BW
YAP, HK
机构
[1] National University of Singapore, Kent Ridge
来源
ARTHRITIS AND RHEUMATISM | 1994年 / 37卷 / 05期
关键词
D O I
10.1002/art.1780370524
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Chronic granulomatous disease (CGD) is an uncommon disorder affecting neutrophil function, and is characterized by recurrent and severe pyogenic infections. Associated autoimmune disorders, in particular lupus-like disorders, are found in carriers of X-linked CGD and in patients with both the X-linked and the autosomal recessive (AR) forms of the disease. We describe a girl with the AR form of CGD and with rheumatoid factor-positive polyarthritis resembling juvenile rheumatoid arthritis. This association has been reported previously only in a single case report of a patient with probable CGD. The present report further substantiates the association between autoimmune phenomena and CGD.
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页码:773 / 776
页数:4
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