HYPERARGININEMIA - EFFECT OF ORNITHINE AND LYSINE SUPPLEMENTATION

被引:20
作者
KANG, SS [1 ]
WONG, PWK [1 ]
MELYN, MA [1 ]
机构
[1] RUSH MED COLL, DEPT PEDIAT, GENET SECT, CHICAGO, IL 60612 USA
关键词
D O I
10.1016/S0022-3476(83)80481-8
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:763 / 765
页数:3
相关论文
共 10 条
[1]   ACCUMULATION OF ORNITHINE AND CITRULLINE IN RAT-LIVER MITOCHONDRIA IN RELATION TO CITRULLINE FORMATION [J].
BRYLA, J ;
HARRIS, EJ .
FEBS LETTERS, 1976, 72 (02) :331-336
[2]   HYPERARGININEMIA [J].
CEDERBAUM, SD ;
SHAW, KNF ;
VALENTE, M .
JOURNAL OF PEDIATRICS, 1977, 90 (04) :569-573
[3]  
CEDERBAUM SD, 1982, J INHERIT METAB DIS, V5, P95, DOI 10.1007/BF01800000
[4]   LYSINE IN TREATMENT OF HYPERORNITHINEMIA [J].
GIORDANO, C ;
DESANTO, NG ;
PLUVIO, M ;
SANTINELLI, R ;
STOPPOLONI, G .
NEPHRON, 1978, 22 (1-3) :97-106
[5]  
MICHELS VV, 1978, CLIN GENET, V13, P61
[6]  
PARDRIDGE WM, 1977, J PEDIATR-US, V91, P1032, DOI 10.1016/S0022-3476(77)80934-7
[7]  
QURESHI IA, 1981, DIABETES METAB, V7, P5
[8]  
SHIH VE, 1979, METABOLIC BASIS INHE, P362
[9]  
SNYDERMAN EE, 1977, J PEDIATR, V91, P1032
[10]   ARGININEMIA [J].
SNYDERMAN, SE ;
SANSARICQ, C ;
CHEN, WJ ;
NORTON, PM ;
PHANSALKAR, SV .
JOURNAL OF PEDIATRICS, 1977, 90 (04) :563-568