IS THERE ANY SPECIFICITY TO DEFECTS OF ANCHORING FIBRILS IN EPIDERMOLYSIS BULLOSA DYSTROPHICA, AND WHAT DOES THIS MEAN IN TERMS OF PATHOGENESIS

被引:39
作者
BRIGGAMAN, RA [1 ]
机构
[1] N CAROLINA MEM HOSP, CHAPEL HILL, NC 27514 USA
关键词
D O I
10.1111/1523-1747.ep12265450
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
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页码:371 / 373
页数:3
相关论文
共 26 条
[1]   EPIDERMOLYSIS BULLOSA DYSTROPHICA DOMINANS - DEFECT OF ANCHORING FIBRILS [J].
ANTONLAMPRECHT, I ;
SCHNYDER, UW .
DERMATOLOGICA, 1973, 147 (05) :289-298
[2]   RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - EVIDENCE FOR AN ALTERED COLLAGENASE IN FIBROBLAST-CULTURES [J].
BAUER, EA .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (10) :4646-4650
[3]   COLCHICINE-INDUCED MODULATION OF COLLAGENASE IN HUMAN-SKIN FIBROBLAST-CULTURES .2. A PROBE FOR DEFECTIVE REGULATION IN EPIDERMOLYSIS BULLOSA [J].
BAUER, EA ;
VALLE, KJ ;
ESTERLY, NB .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1982, 79 (06) :403-407
[4]   RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA - EVIDENCE FOR INCREASED COLLAGENASE AS A GENETIC CHARACTERISTIC IN CELL-CULTURE [J].
BAUER, EA ;
EISEN, AZ .
JOURNAL OF EXPERIMENTAL MEDICINE, 1978, 148 (05) :1378-1387
[5]   ROLE OF HUMAN-SKIN COLLAGENASE IN EPIDERMOLYSIS BULLOSA [J].
BAUER, EA ;
GEDDEDAHL, T ;
EISEN, AZ .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1977, 68 (03) :119-124
[6]   INCREASED GLYCOSAMINOGLYCAN ACCUMULATION AS A GENETIC CHARACTERISTIC IN CELL-CULTURES OF ONE VARIETY OF DOMINANT DYSTROPHIC EPIDERMOLYSIS BULLOSA [J].
BAUER, EA ;
FIEHLER, WK ;
ESTERLY, NB .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (01) :32-39
[7]  
BAUER EA, 1982, J INVEST DERMATOL S, V75, pS105
[8]   ISOLATION AND PARTIAL CHARACTERIZATION OF A NEW HUMAN COLLAGEN WITH AN EXTENDED TRIPLE-HELICAL STRUCTURAL DOMAIN [J].
BENTZ, H ;
MORRIS, NP ;
MURRAY, LW ;
SAKAI, LY ;
HOLLISTER, DW ;
BURGESON, RE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (11) :3168-3172
[9]   EPIDERMOLYSIS BULLOSA DYSTROPHICA RECESSIVE - POSSIBLE ROLE OF ANCHORING FIBRILS IN PATHOGENESIS [J].
BRIGGAMAN, RA ;
WHEELER, CE .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1975, 65 (02) :203-211
[10]  
EHRLICH HP, 1983, J INVEST DERMATOL, V81, P572, DOI 10.1111/1523-1747.ep12523260