NEW PATHOLOGICAL OBSERVATIONS IN JUVENILE ONSET PARKINSONISM WITH DYSTONIA

被引：51

作者：

GIBB, WRG

NARABAYASHI, H

YOKOCHI, M

IIZUKA, R

LEES, AJ

机构：

[1] NATL HOSP,LONDON WC1N 3BG,ENGLAND

[2] JUNTENDO UNIV,SCH MED,DEPT NEUROL,TOKYO 113,JAPAN

来源：

NEUROLOGY | 1991年 / 41卷 / 06期

关键词：

D O I：

10.1212/WNL.41.6.820

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

A patient with hereditary juvenile onset parkinsonism with dystonia died at age 39. There were Lewy bodies and regionally selective neuronal damage in the substantia nigra pars compacta. These changes closely resemble those seen in Parkinson's disease, and emphasize the selective vulnerability of the ventral tier of the pars compacta in these degenerations.

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页码：820 / 822

页数：3

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