ACCUMULATION OF PHOSPHORYLATED DOLICHOL IN SEVERAL TISSUES IN CEROID-LIPOFUSCINOSIS (BATTEN DISEASE)

被引:17
作者
HALL, NA
PATRICK, AD
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关键词
D O I
10.1016/0009-8981(87)90143-4
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
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页码:323 / 330
页数:8
相关论文
共 9 条
[1]  
ADAIR WL, 1985, METHOD ENZYMOL, V111, P201
[2]  
CARSON DD, 1981, J BIOL CHEM, V256, P4679
[3]   DOLICHOL AND PHOSPHORYLATED DOLICHOL CONTENT OF TISSUES IN CEROID-LIPOFUSCINOSIS [J].
HALL, NA ;
PATRICK, AD .
JOURNAL OF INHERITED METABOLIC DISEASE, 1985, 8 (04) :178-183
[4]  
KELLER RK, 1984, J NEUROCHEM, V42, P1040, DOI 10.1111/j.1471-4159.1984.tb12708.x
[5]   HIGH-LEVELS OF BRAIN DOLICHOLS IN NEURONAL CEROID-LIPOFUSCINOSIS AND SENESCENCE [J].
KIN, NMKNY ;
PALO, J ;
HALTIA, M ;
WOLFE, LS .
JOURNAL OF NEUROCHEMISTRY, 1983, 40 (05) :1465-1473
[6]  
McKusick V.A., 1983, MENDELIAN INHERITANC
[7]   AGE-ASSOCIATED INCREASE OF FREE DOLICHOL LEVELS IN MICE [J].
PULLARKAT, RK ;
REHA, H ;
PULLARKAT, PS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1984, 793 (03) :494-496
[8]   DOLICHOL IN HUMAN-BRAIN - REGIONAL AND DEVELOPMENTAL ASPECTS [J].
SAKAKIHARA, Y ;
VOLPE, JJ .
JOURNAL OF NEUROCHEMISTRY, 1985, 44 (05) :1535-1540
[9]  
WOLFE LS, 1982, BIRTH DEFECTS-ORIG, V18, P233