PLASMA BILE-ACIDS IN PATIENTS WITH PEROXISOMAL DYSFUNCTION SYNDROMES - ANALYSIS BY CAPILLARY GAS-CHROMATOGRAPHY MASS-SPECTROMETRY

被引:42
作者
CLAYTON, PT
LAKE, BD
HALL, NA
SHORTLAND, DB
CARRUTHERS, RA
LAWSON, AM
机构
[1] HOSP SICK CHILDREN,LONDON WC1N 3JH,ENGLAND
[2] QUEENS MED CTR,SCH MED,DEPT CHILD HLTH,NOTTINGHAM NG7 2UH,ENGLAND
[3] CLIN RES CTR,HARROW HA1 3UJ,MIDDX,ENGLAND
关键词
D O I
10.1007/BF02343226
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:166 / 173
页数:8
相关论文
共 34 条
[1]   SEPARATION AND COMPUTERIZED GAS CHROMATOGRAPHY MASS SPECTROMETRY OF UNCONJUGATED NEUTRAL STEROIDS IN PLASMA [J].
AXELSON, M ;
SJOVALL, J .
JOURNAL OF STEROID BIOCHEMISTRY AND MOLECULAR BIOLOGY, 1974, 5 (08) :733-738
[2]   PHENOBARBITAL-INDUCED ALTERATIONS OF BILE-ACID METABOLISM IN CASES OF INTRA-HEPATIC CHOLESTASIS [J].
BACK, P .
KLINISCHE WOCHENSCHRIFT, 1982, 60 (11) :541-549
[3]  
BACK P, 1978, INN MED, V5, P329
[4]   A MILDER VARIANT OF ZELLWEGER SYNDROME [J].
BARTH, PG ;
SCHUTGENS, RBH ;
BAKKEREN, JAJM ;
DINGEMANS, KP ;
HEYMANS, HSA ;
DOUWES, AC ;
VANDERKLEIVANMOORSEL, JM .
EUROPEAN JOURNAL OF PEDIATRICS, 1985, 144 (04) :338-342
[5]  
BLEEKERWAGEMAKERS EM, 1986, CLIN GENET, V29, P160
[6]   THE BILE-ACID COMPOSITION OF GASTRIC CONTENTS FROM NEONATES WITH HIGH INTESTINAL-OBSTRUCTION [J].
CLAYTON, PT ;
MULLER, DPR ;
LAWSON, AM .
BIOCHEMICAL JOURNAL, 1982, 206 (03) :489-498
[7]   A SIMPLIFIED GAS-LIQUID-CHROMATOGRAPHIC METHOD FOR THE ESTIMATION OF NON-SULFATED PLASMA BILE-ACIDS [J].
CLAYTON, PT ;
MULLER, DPR .
CLINICA CHIMICA ACTA, 1980, 105 (03) :401-405
[8]  
CLAYTON PT, 1984, THESIS U CAMBRIDGE
[9]   PHENACYL ESTERS OF FATTY-ACIDS VIA CROWN ETHER CATALYSTS FOR ENHANCED ULTRAVIOLET DETECTION IN LIQUID-CHROMATOGRAPHY [J].
DURST, HD ;
MILANO, M ;
KIKTA, EJ ;
CONNELLY, SA ;
GRUSHKA, E .
ANALYTICAL CHEMISTRY, 1975, 47 (11) :1797-1801
[10]   BILE-ACID ABNORMALITIES AND THE DIAGNOSIS OF CEREBRO-HEPATO-RENAL SYNDROME (ZELLWEGER SYNDROME) [J].
EYSSEN, H ;
EGGERMONT, E ;
VANELDERE, J ;
JAEKEN, J ;
PARMENTIER, G ;
JANSSEN, G .
ACTA PAEDIATRICA SCANDINAVICA, 1985, 74 (04) :539-544