EXOCRINE PANCREATIC INSUFFICIENCY IN SYNDROMIC PAUCITY OF INTERLOBULAR BILE-DUCTS

被引:25
作者
CHONG, SKF
LINDRIDGE, J
MONIZ, C
MOWAT, AP
机构
[1] UNIV LONDON KINGS COLL HOSP,DEPT CHILD HLTH,LONDON SE5 8RX,ENGLAND
[2] UNIV LONDON KINGS COLL HOSP,DEPT CHEM PATHOL,LONDON SE5 8RX,ENGLAND
关键词
D O I
10.1097/00005176-198911000-00009
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:445 / 449
页数:5
相关论文
共 11 条
[1]   SYNDROMIC PAUCITY OF INTERLOBULAR BILE-DUCTS (ALAGILLE SYNDROME OR ARTERIOHEPATIC DYSPLASIA) - REVIEW OF 80 CASES [J].
ALAGILLE, D ;
ESTRADA, A ;
HADCHOUEL, M ;
GAUTIER, M ;
ODIEVRE, M ;
DOMMERGUES, JP .
JOURNAL OF PEDIATRICS, 1987, 110 (02) :195-200
[2]  
BARBEZAT GO, 1968, PEDIATRICS, V42, P77
[3]   SYNDROMIC PAUCITY OF THE INTRAHEPATIC BILE-DUCTS - DIAGNOSTIC DIFFICULTY - SEVERE MORBIDITY THROUGHOUT EARLY-CHILDHOOD [J].
DEPRETTERE, A ;
PORTMANN, B ;
MOWAT, AP .
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1987, 6 (06) :865-871
[4]  
JAIN MK, 1986, DIARRHOEA MALNUTRITI, P142
[5]  
JOHANSEN AJ, 1971, J PEDIATR, V75, P982
[6]   ON THE PROBABLE INVOLVEMENT OF ARGININE RESIDUES IN THE BILE-SALT-BINDING SITE OF HUMAN PANCREATIC CARBOXYLIC ESTER HYDROLASE [J].
LOMBARDO, D ;
CAMPESE, D ;
MULTIGNER, L ;
LAFONT, H ;
DECARO, A .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1983, 133 (02) :327-333
[7]  
MOWAT AP, 1987, LIVER DISORDERS CHIL, P64
[8]   STABILITY OF PANCREATIC-ENZYME ACTIVITIES IN DUODENAL JUICE AFTER PANCREATIC STIMULATION BY A TEST MEAL OR EXOGENOUS HORMONES [J].
MULLER, DPR ;
GHALE, GK .
ANNALS OF CLINICAL BIOCHEMISTRY, 1982, 19 (MAR) :89-93
[9]  
SCHUSSHEIM A, 1978, J PEDIATR, V6, P782
[10]   COMPETITIVE INHIBITORY EFFECT EXERTED BY BILE-SALT MICELLES ON HYDROLYSIS OF TRIBUTYRIN BY PANCREATIC LIPASE [J].
VANDERMEERS, A ;
VANDERMEERSPIRET, MC ;
RATHE, J ;
CHRISTOPHE, J .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1976, 69 (03) :790-797