LIVER ULTRASTRUCTURE IN MITOCHONDRIAL UREA CYCLE ENZYME DEFICIENCIES AND COMPARISON WITH REYES-SYNDROME

被引：15

作者：

LATHAM, PS

LABRECQUE, DR

MCREYNOLDS, JW

KLATSKIN, G

机构：

[1] VET ADM MED CTR,BALTIMORE,MD 21218

[2] UNIV IOWA,IOWA CITY,IA 52242

[3] VET ADM MED CTR,IOWA CITY,IA 52240

[4] UNIV FLORIDA,COLL MED,GAINESVILLE,FL 32610

[5] YALE UNIV,SCH MED,NEW HAVEN,CT 06510

来源：

HEPATOLOGY | 1984年 / 4卷 / 03期

关键词：

D O I：

10.1002/hep.1840040308

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

引用

页码：404 / 407

页数：4

共 12 条

[1] 2 MORPHOLOGICALLY DIFFERENT MITOCHONDRIAL POPULATIONS IN RAT HEPATOCYTE AS DETERMINED BY QUANTITATIVE 3-DIMENSIONAL ELECTRON-MICROSCOPY [J].

BERGER, ER .

JOURNAL OF ULTRASTRUCTURE RESEARCH, 1973, 45 (5-6) :303-327

[2] MICROBODIES IN THE LIVING CELL [J].

DEDUVE, C .

SCIENTIFIC AMERICAN, 1983, 248 (05) :74-84

[3]

FAWCETT DW, 1955, J NATL CANCER I, V15, P1475

[4] HYPERORNITHINEMIA, HYPERAMMONEMIA, AND HOMOCITRULLINURIA ASSOCIATED WITH DECREASED CARBAMYL-PHOSPHATE SYNTHETASE-I ACTIVITY [J].

GATFIELD, PD ;

TALLER, E ;

WOLFE, DM ;

HAUST, MD .

PEDIATRIC RESEARCH, 1975, 9 (05) :488-497

[5] ULTRASTRUCTURAL BASES FOR METABOLICALLY LINKED MECHANICAL ACTIVITY IN MITOCHONDRIA .I. REVERSIBLE ULTRASTRUCTURAL CHANGES WITH CHANGE IN METABOLIC STEADY STATE IN ISOLATED LIVER MITOCHONDRIA [J].

HACKENBROCK, CR .

JOURNAL OF CELL BIOLOGY, 1966, 30 (02) :269-+

[6] HERITABLE UREA CYCLE ENZYME DEFICIENCY - LIVER-DISEASE IN 16 PATIENTS [J].

LABRECQUE, DR ;

LATHAM, PS ;

RIELY, CA ;

HSIA, YE ;

KLATSKIN, G .

JOURNAL OF PEDIATRICS, 1979, 94 (04) :580-587

[7] TREATMENT OF COMPLETE ORNITHINE TRANSCARBAMYLASE DEFICIENCY WITH NITROGEN-FREE ANALOGS OF ESSENTIAL AMINO-ACIDS [J].

MCREYNOLDS, JW ;

MANTAGOS, S ;

BRUSILOW, S ;

ROSENBERG, LE .

JOURNAL OF PEDIATRICS, 1978, 93 (03) :421-427

[8]

MCREYNOLDS JW, 1981, AM J HUM GENET, V33, P345

[9] MITOCHONDRIAL ULTRASTRUCTURE IN REYES SYNDROME (ENCEPHALOPATHY AND FATTY DEGENERATION OF VISCERA) [J].

PARTIN, JC ;

SCHUBERT, WK ;

PARTIN, JS .

NEW ENGLAND JOURNAL OF MEDICINE, 1971, 285 (24) :1339-&

[10] MITOCHONDRIAL ABNORMALITIES OF LIVER IN PRIMARY ORNITHINE TRANSCARBAMYLASE DEFICIENCY [J].

SHAPIRO, JM ;

SCHAFFNER, F ;

TALLAN, HH ;

GAULL, GE .

PEDIATRIC RESEARCH, 1980, 14 (05) :735-739

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