CYSTEAMINE THERAPY FOR CHILDREN WITH NEPHROPATHIC CYSTINOSIS

被引：237

作者：

GAHL, WA

REED, GF

THOENE, JG

SCHULMAN, JD

RIZZO, WB

JONAS, AJ

DENMAN, DW

SCHLESSELMAN, JJ

CORDEN, BJ

SCHNEIDER, JA

机构：

[1] NICHHD, BIOMETRY BRANCH, BETHESDA, MD 20892 USA

[2] UNIV MICHIGAN, DEPT PEDIAT, ANN ARBOR, MI 48109 USA

[3] UNIV MICHIGAN, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA

[4] UNIV CALIF SAN DIEGO, DEPT PEDIAT, LA JOLLA, CA 92093 USA

来源：

NEW ENGLAND JOURNAL OF MEDICINE | 1987年 / 316卷 / 16期

关键词：

D O I：

10.1056/NEJM198704163161602

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：971 / 977

页数：7

共 38 条

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[3] Broyer M, 1981, Adv Nephrol Necker Hosp, V10, P137
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[7] INVIVO USE OF DITHIOTHREITOL IN CYSTINOSIS
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[8] Gahl W A, 1986, Adv Pediatr, V33, P95
[9] CHARACTERISTICS OF CYSTINE COUNTER-TRANSPORT IN NORMAL AND CYSTINOTIC LYSOSOME-RICH LEUKOCYTE GRANULAR FRACTIONS
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[J]. BIOCHEMICAL JOURNAL, 1983, 216 (02) : 393 - 400
[10] BLUNTED PROLACTIN RESPONSE TO THYROTROPIN-RELEASING-HORMONE STIMULATION IN CYSTINOTIC CHILDREN RECEIVING CYSTEAMINE
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[J]. JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1985, 60 (04) : 793 - 796

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