NEUROCHEMICAL CHARACTERIZATION OF CANINE ALPHA-L-IDURONIDASE DEFICIENCY DISEASE (MODEL OF HUMAN MUCOPOLYSACCHARIDOSIS-I)

被引：16

作者：

CONSTANTOPOULOS, G

SHULL, RM

HASTINGS, N

NEUFELD, EF

机构：

[1] NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA

[2] UNIV TENNESSEE, COLL VET MED, DEPT PATHOBIOL, KNOXVILLE, TN 37996 USA

来源：

JOURNAL OF NEUROCHEMISTRY | 1985年 / 45卷 / 04期

关键词：

D O I：

10.1111/j.1471-4159.1985.tb05544.x

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：1213 / 1217

页数：5

共 18 条

[1] NEW METHOD FOR QUANTITATIVE-DETERMINATION OF URONIC ACIDS [J].

BLUMENKR.N ;

ASBOEHAN.G .

ANALYTICAL BIOCHEMISTRY, 1973, 54 (02) :484-489

[2]

BREEN M, 1976, METHODS CARBOHYDRATE, V7, P101

[3] NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN GLYCOSAMINOGLYCANS IN NORMALS AND 4 TYPES OF MUCOPOLYSACCHARIDOSES [J].

CONSTANTOPOULOS, G ;

MCCOMB, RD ;

DEKABAN, AS .

JOURNAL OF NEUROCHEMISTRY, 1976, 26 (05) :901-&

[4] DETERMINATION OF MOLECULAR WEIGHT DISTRIBUTION OF ACID MUCOPOLYSACCHARIDES BY SEPHADEX GEL FILTRATION [J].

CONSTANTOPOULOS, G ;

DEKABAN, AS ;

CARROLL, WR .

ANALYTICAL BIOCHEMISTRY, 1969, 31 (1-3) :59-+

[5] NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN LIPIDS AND LYSOSOMAL ENZYMES IN PATIENTS WITH 4 TYPES OF MUCOPOLYSACCHARIDOSIS AND IN NORMAL CONTROLS [J].

CONSTANTOPOULOS, G ;

DEKABAN, AS .

JOURNAL OF NEUROCHEMISTRY, 1978, 30 (05) :965-973

[6] MUCOPOLYSACCHARIDOSIS TYPE-IH, TYPE-IS, TYPE-II, AND TYPE-IIIA - GLYCOSAMINOGLYCANS AND LIPIDS OF ISOLATED BRAIN-CELLS AND OTHER FRACTIONS FROM AUTOPSIED TISSUES [J].

CONSTANTOPOULOS, G ;

IQBAL, K ;

DEKABAN, AS .

JOURNAL OF NEUROCHEMISTRY, 1980, 34 (06) :1399-1411

[7] MUCOPOLYSACCHARIDOSES - RELATION OF ELEVATED CEREBRAL SPINAL-FLUID TO MENTAL-RETARDATION [J].

DEKABAN, AS ;

CONSTANTOPOULOS, G .

ARCHIVES OF NEUROLOGY, 1973, 28 (06) :385-388

[8]

FOLCH J, 1957, J BIOL CHEM, V226, P497

[9]

Haskins M E, 1982, Prog Clin Biol Res, V94, P177

[10] ALPHA-L-IDURONIDASE DEFICIENCY IN A CAT - MODEL OF MUCOPOLYSACCHARIDOSIS-I [J].

HASKINS, ME ;

JEZYK, PF ;

DESNICK, RJ ;

MCDONOUGH, SK ;

PATTERSON, DF .

PEDIATRIC RESEARCH, 1979, 13 (11) :1294-1297

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