PYROGLUTAMIC ACIDURIA IN PROPIONYL COA CARBOXYLASE DEFICIENCY

被引:9
作者
MORISHITA, H
NAGAYA, S
NAKAJIMA, T
KAWASE, A
OHYA, A
SUGIYAMA, S
KAMIYA, K
WATANABE, I
TOGARI, H
SUZUKI, Y
KOBAYASHI, M
OGAWA, Y
WADA, Y
HOKAZONO, Y
SUGIYAMA, N
机构
[1] SEIREI HAMAMATSU HOSP,DEPT PEDIAT,HAMAMATSU 430,JAPAN
[2] AICHI GAKUIN UNIV,SCH DENT,DEPT MED & PEDIAT,CHIKUSA KU,NAGOYA 464,JAPAN
关键词
D O I
10.1007/BF01801776
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:139 / 140
页数:2
相关论文
共 7 条
  • [1] GRAVEL RA, 1977, AM J HUM GENET, V29, P378
  • [2] COMBINED SYSTEM FOR THE STUDY OF GLUTATHIONE METABOLISM IN ERYTHROCYTES
    ISHIDA, Y
    NAKASHIMA, K
    FUJII, H
    MIWA, S
    [J]. CLINICA CHIMICA ACTA, 1979, 93 (03) : 381 - 389
  • [3] ENZYMOLOGY OF AMINO-ACID TRANSPORT
    MEISTER, A
    [J]. SCIENCE, 1973, 180 (4081) : 33 - 39
  • [4] HIGHLY EFFICIENT CARBOXYLIC-ACID ANALYZER AND ITS APPLICATION
    NAKAJIMA, M
    OZAWA, Y
    TANIMURA, T
    TAMURA, Z
    [J]. JOURNAL OF CHROMATOGRAPHY, 1976, 123 (01): : 129 - 138
  • [5] INTERMEDIATES OF GAMMA-GLUTAMYL CYCLE IN MOUSE TISSUES - INFLUENCE OF ADMINISTRATION OF AMINO-ACIDS ON PYRROLIDONE CARBOXYLATE AND GAMMA-GLUTAMYL AMINO-ACIDS
    ORLOWSKI, M
    WILK, S
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1975, 53 (02): : 581 - 590
  • [6] UTTER MF, 1963, J BIOL CHEM, V238, P2603
  • [7] DEFICIENCY OF PROPIONYL-COA CARBOXYLASE AND METHYLCROTONYL-COA CARBOXYLASE IN A PATIENT WITH METHYLCROTONYLGLYCINURIA
    WEYLER, W
    SWEETMAN, L
    MAGGIO, DC
    NYHAN, WL
    [J]. CLINICA CHIMICA ACTA, 1977, 76 (03) : 321 - 328