FAMILIAL AGGREGATION OF CANCER FROM PROBAND CASES WITH CHILDHOOD ADRENAL-CORTICAL CARCINOMA

被引:14
作者
TSUNEMATSU, Y
WATANABE, S
OKA, T
TSUKAMOTO, T
KEISEI, KH
HIRATA, Y
YAMANAKA, H
OHIRA, M
ONO, M
机构
[1] NATL CANC CTR,RES INST,CHUO KU,TOKYO 104,JAPAN
[2] ASAHIKAWA MED COLL,ASAHIKAWA,HOKKAIDO 078,JAPAN
[3] OSAKA UNIV HOSP,FUKUSHIMA KU,OSAKA 553,JAPAN
[4] SAPPORO MED COLL,CHUO KU,SAPPORO,HOKKAIDO 060,JAPAN
[5] HAMAMATSU MED CTR,HAMAMATSU,SHIZUOKA 431,JAPAN
[6] AICHI MED UNIV,AICHI 48011,JAPAN
[7] TOKYO NTT HOSP,CHIYODA KU,TOKYO 122,JAPAN
来源
JAPANESE JOURNAL OF CANCER RESEARCH | 1991年 / 82卷 / 08期
关键词
LI-FRAUMENI SYNDROME; ADRENOCORTICAL CANCER; BREAST CANCER; EPIDEMIOLOGY;
D O I
10.1111/j.1349-7006.1991.tb01918.x
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Family pedigree of Li-Fraumeni syndrome was investigated from probands with childhood adrenocortical carcinoma in Japan. From 47 probands, 7 families had 3 or more cancer cases at ages less than 45 years within the first generation; one satisfied Li's original criteria, two were acceptable because of multiple primary cancer in the probands, and others showed an aggregation of cancers with onsets at early ages, though no sarcoma of mescenchymal origin was found. A significantly higher occurrence of cancer in the mothers of the probands, especially of the breast, was consistent with reports from the USA, and liver cancer, osteosarcoma and lung cancer among family members under the age of 45 also showed a higher frequency than in the general population. Similarities and differences between Japanese and Caucasian cases are discussed.
引用
收藏
页码:893 / 900
页数:8
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