DEFICIENCY OF ARGININE ESTERASE IN CYSTIC-FIBROSIS OF PANCREAS - DEMONSTRATION OF PROTEOLYTIC NATURE OF ACTIVITY

被引:32
作者
RAO, GJS [1 ]
NADLER, HL [1 ]
机构
[1] NORTHWESTERN UNIV,CHILDRENS MEM HOSP,MED SCH,DEPT PEDIAT,DIV GENET,CHICAGO,IL 60201
关键词
D O I
10.1203/00006450-197509000-00011
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:739 / 741
页数:3
相关论文
共 18 条
[1]  
BARNETT DR, 1973, TEX REP BIOL MED, V31, P697
[2]  
BARNETT DR, 1973, TEX REP BIOL MED, V31, P703
[3]   HUMAN CATHEPSIN-B1 - PURIFICATION AND SOME PROPERTIES OF ENZYME [J].
BARRETT, AJ .
BIOCHEMICAL JOURNAL, 1973, 131 (04) :809-+
[4]   CYSTIC FIBROSIS . CHARACTERIZATION OF INHIBITOR TO CILIARY ACTION IN OYSTER GILLS [J].
BOWMAN, BH ;
MCCOMBS, ML ;
LOCKHART, LH .
SCIENCE, 1970, 167 (3919) :871-&
[5]   SENSITIVE FLUORESCENT DETERMINATION OF TRYPSIN-LIKE PROTEASES [J].
BROWN, F ;
FREEDMAN, ML ;
TROLL, W .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1973, 53 (01) :75-81
[6]   COMPARISON OF ESTERASE ACTIVITIES OF TRYPSIN PLASMIN AND THROMBIN ON GUANIDINOBENZOATE ESTERS . TITRATION OF ENZYMES [J].
CHASE, T ;
SHAW, E .
BIOCHEMISTRY, 1969, 8 (05) :2212-&
[7]   STUDIES ON PREKALLIKREIN (KALLIKREINOGEN)-KALLIKREIN ENZYME SYSTEM OF HUMAN PLASMA .2. EVIDENCE RELATING KAOLIN-ACTIVATED ARGININE ESTERASE TO PLASMA KALLIKREIN [J].
COLMAN, RW ;
MATTLER, L ;
SHERRY, S .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (01) :23-&
[8]   STUDIES ON CILIARY DYSKINESIA FACTOR IN CYSTIC-FIBROSIS .4. ITS POSSIBLE IDENTIFICATION AS ANAPHYLATOXIN (C3A)-IGG COMPLEX [J].
CONOVER, JH ;
CONOD, EJ ;
HIRSCHHORN, K .
LIFE SCIENCES, 1974, 14 (02) :253-266
[9]  
GLOVER G, 1971, J BIOL CHEM, V246, P4594
[10]  
GROSKOPF WR, 1969, J BIOL CHEM, V244, P359