BIOCHEMICAL INVESTIGATIONS OF DIFFERENT FORMS OF OSTEOGENESIS IMPERFECTA - EVALUATION OF 44 CASES

被引:26
作者
CETTA, G [1 ]
DELUCA, G [1 ]
TENNI, R [1 ]
ZANABONI, G [1 ]
LENZI, L [1 ]
CASTELLANI, AA [1 ]
机构
[1] UNIV PAVIA,FAC MED & CHIRURG,IST CHIM BIOL,I-27100 PAVIA,ITALY
关键词
D O I
10.3109/03008208309004847
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
引用
收藏
页码:103 / 111
页数:9
相关论文
共 19 条
[1]  
ASKENASI R, 1976, METHODOLOGY CONNECTI, P263
[2]  
CETTA G, 1980, ITAL J BIOCHEM, V29, P337
[3]  
CETTA G, 1979, ITAL J BIOCHEM, V28, P163
[4]   BIOCHEMICAL AND MORPHOLOGICAL MODIFICATIONS IN RABBIT ACHILLES-TENDON DURING MATURATION AND AGING [J].
CETTA, G ;
TENNI, R ;
ZANABONI, G ;
DELUCA, G ;
IPPOLITO, E ;
DEMARTINO, C ;
CASTELLANI, AA .
BIOCHEMICAL JOURNAL, 1982, 204 (01) :61-&
[5]  
COLE WG, 1981, CONNECT TISSUE RES, V8, P136
[6]   MEASUREMENT OF URINARY MUCOPOLYSACCHARIDES [J].
DIFERRAN.NM .
ANALYTICAL BIOCHEMISTRY, 1967, 21 (01) :98-&
[7]   COMPARATIVE-STUDY OF CARBOHYDRATE-PROTEIN COMPLEXES .2. DETERMINATION OF HYDROXYLYSINE AND ITS GLYCOSIDES IN HUMAN-SKIN AND SCAR COLLAGENS BY AN IMPROVED METHOD [J].
ISEMURA, M ;
TAKAHASHI, K ;
IKENAKA, T .
JOURNAL OF BIOCHEMISTRY, 1976, 80 (04) :653-658
[8]   DISORDER OF COLLAGEN-METABOLISM IN A PATIENT WITH OSTEOGENESIS IMPERFECTA (LETHAL TYPE) - INCREASED DEGREE OF HYDROXYLATION OF LYSINE IN COLLAGEN TYPE-I AND TYPE-III [J].
KIRSCH, E ;
KRIEG, T ;
REMBERGER, K ;
FENDEL, H ;
BRUCKNER, P ;
MULLER, PK .
EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, 1981, 11 (01) :39-47
[9]   OSTEOGENESIS IMPERFECTA - BIOCHEMICAL AND CLINICAL-EVALUATION OF 13 CASES [J].
KRIEG, T ;
KIRSCH, E ;
MATZEN, K ;
MULLER, PK .
KLINISCHE WOCHENSCHRIFT, 1981, 59 (02) :91-93
[10]   DOMINANTLY INHERITED OSTEOGENESIS IMPERFECTA IN MAN - EXAMINATION OF COLLAGEN BIOSYNTHESIS [J].
LANCASTER, G ;
GOLDMAN, H ;
SCRIVER, CR ;
GOLD, RJM ;
WONG, I .
PEDIATRIC RESEARCH, 1975, 9 (02) :83-88