ORTHOTOPIC LIVER-TRANSPLANTATION FOR CHOLESTERYL ESTER STORAGE DISEASE

被引:18
作者
ARTERBURN, JN
LEE, WM
WOOD, RP
SHAW, BW
MARKIN, RS
机构
[1] UNIV NEBRASKA,MED CTR,DEPT SURG,OMAHA,NE 68105
[2] UNIV NEBRASKA,MED CTR,DEPT PATHOL,OMAHA,NE 68105
关键词
D O I
10.1097/00004836-199108000-00028
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:482 / 485
页数:4
相关论文
共 8 条
[1]  
ASHMANN G, 1983, METABOLIC BASIS INHE, P803
[2]  
EDELSTEIN RA, 1988, AM J GASTROENTEROL, V83, P687
[3]   NEWLY RECOGNIZED DISORDERS OF CHOLESTEROL METABOLISM [J].
FREDRICKSON, DS .
ANNALS OF INTERNAL MEDICINE, 1963, 58 (04) :718-+
[4]   ASSIGNMENT OF LIPA, ASSOCIATED WITH HUMAN ACID LIPASE DEFICIENCY, TO HUMAN CHROMOSOME-10 AND COMPARATIVE ASSIGNMENT TO MOUSE CHROMOSOME-19 [J].
KOCH, G ;
LALLEY, PA ;
MCAVOY, M ;
SHOWS, TB .
SOMATIC CELL GENETICS, 1981, 7 (03) :345-358
[5]   CHOLESTERYL ESTER STORAGE DISEASE - REPORT ON 4 CASES [J].
PFEIFER, U ;
JESCHKE, R .
VIRCHOWS ARCHIV B-CELL PATHOLOGY INCLUDING MOLECULAR PATHOLOGY, 1980, 33 (01) :17-34
[6]   ENZYME REPLACEMENT THERAPY IN FIBROBLASTS FROM A PATIENT WITH CHOLESTERYL ESTER STORAGE DISEASE [J].
POZNANSKY, MJ ;
HUTCHISON, SK ;
DAVIS, PJ .
FASEB JOURNAL, 1989, 3 (02) :152-156
[7]   LIVER-TRANSPLANTATION .1. [J].
STARZL, TE ;
DEMETRIS, AJ ;
VANTHIEL, D .
NEW ENGLAND JOURNAL OF MEDICINE, 1989, 321 (15) :1014-1022
[8]  
STARZL TE, 1989, SURGERY LIVER, P127