ANGIOIMMUNOBLASTIC LYMPHADENOPATHY MIMICKING DERMATITIS-HERPETIFORMIS (DUHRINGS-DISEASE)

被引:8
作者
ZUMDICK, M [1 ]
MEGAHED, M [1 ]
BORCHARD, F [1 ]
WOHDE, D [1 ]
GOERZ, G [1 ]
机构
[1] HEINRICHG HEINE UNIV,INST PATHOL,DUSSELDORF,GERMANY
来源
HAUTARZT | 1994年 / 45卷 / 08期
关键词
ANGIOIMMUNOBLASTIC LYMPHADENOPATHY; BULLOUS SKIN LESIONS; DERMATITIS-HERPETIFORMIS DUHRINGS DISEASE;
D O I
10.1007/s001050050127
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A 62-year-old female patient presented with bullous, intensely itching cutaneous lesions, which clinically and histopathologically resembled dermatitis herpetiformis (Duhring's disease). Therapy with DADPS was unsuccessful. Because of associated cervical lymph node enlargement and splenomegaly, a lymph node biopsy was taken. Histopathology of a lymph node and of the bone marrow confirmed the diagnosis: angioimmunoblastic lymphadenopathy (AILD)-type T-cell lymphoma. Intensely pruritic associated skin eruptions are typical for this peculiar kind of lymphoma. These skin lesions are due to inflammatory cells and not to neoplastic infiltrations. This case report is the first report of AILD with bullous skin lesions to appear in the literature.
引用
收藏
页码:562 / 565
页数:4
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