ESTIMATES OF URIDINE-DIPHOSPHATE HEXOSES IN ERYTHROCYTES - IMPLICATIONS FOR GALACTOSEMIA

被引:5
作者
KIRKMAN, HN [1 ]
CLEMONS, EH [1 ]
机构
[1] UNIV N CAROLINA, SCH MED, DEPT PEDIAT & BRAIN, CHAPEL HILL, NC 27599 USA
关键词
D O I
10.1016/S0022-3476(06)80127-7
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Impurities in a reagent dehydrogenase caused overestimates of erythrocytic uridine diphosphate glucose and accounted for clinically important differences in results between those of one group of investigators using enzymatic methods and those of two other groups using enzymatic methods, high-performance liquid chromatography, and nuclear magnetic resonance. These data have relevance for the current debate regarding the pathophysiologic changes in galactosemia.
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页码:257 / 259
页数:3
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