HEXOSAMINIDASE A DEFICIENT ADULTS - PRESENCE OF ALPHA-CHAIN PRECURSOR IN CULTURED SKIN FIBROBLASTS

被引：15

作者：

FRISCH, A

BARAM, D

NAVON, R

机构：

[1] TEL AVIV UNIV,SACKLER FAC MED,DEPT HUMAN GENET,TEL HASHOMER,ISRAEL

[2] CHAIM SHEBA MED CTR,IL-52621 TEL HASHOMER,ISRAEL

来源：

关键词：

D O I：

10.1016/0006-291X(84)91624-3

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：101 / 107

页数：7

共 9 条

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[7] SYNTHESIS OF BETA-HEXOSAMINIDASE IN CELL-FREE TRANSLATION AND IN INTACT FIBROBLASTS - AN INSOLUBLE PRECURSOR ALPHA-CHAIN IN A RARE FORM OF TAY-SACHS DISEASE
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