HETEROTOPIC LIVER-TRANSPLANTATION FOR FULMINANT WILSONS-DISEASE

被引:37
作者
STAMPFL, DA
MUNOZ, SJ
MORITZ, MJ
RUBIN, R
ARMENTI, VT
JARRELL, BE
MADDREY, WC
机构
[1] THOMAS JEFFERSON UNIV,JEFFERSON MED COLL,DEPT MED,1025 WALNUT ST,PHILADELPHIA,PA 19107
[2] THOMAS JEFFERSON UNIV,JEFFERSON MED COLL,DEPT SURG,PHILADELPHIA,PA 19107
[3] THOMAS JEFFERSON UNIV,JEFFERSON MED COLL,DEPT PATHOL,PHILADELPHIA,PA 19107
关键词
D O I
10.1016/0016-5085(90)90497-O
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Wilson's disease may present with severe acute hepatocellular failure. The only effective treatment for fulminant Wilson's disease is liver transplantation, which may lead to reversal of the underlying disease. Some patients with cirrhosis who are too ill to undergo orthotopic liver transplantation have been treated with heterotopic liver transplantation. However, use of heterotopic liver transplantation for fulminant hepatocellular failure has not been successful. This case study involves a patient in whom a heterotopic liver transplant was successfully used for treatment of Wilson's disease presenting with fulminant hepatocellular failure. © 1990.
引用
收藏
页码:1834 / 1836
页数:3
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