INTRALYSOSOMAL FORMATION AND METABOLIC-FATE OF N-ACETYLGLUCOSAMINE 6-SULFATE FROM KERATAN SULFATE

被引:13
作者
FUCHS, W [1 ]
BECK, M [1 ]
KRESSE, H [1 ]
机构
[1] UNIV MUNSTER,INST PHYSIOL CHEM,WALDEYERSTR 15,D-4400 MUNSTER,FED REP GER
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1985年 / 151卷 / 03期
关键词
D O I
10.1111/j.1432-1033.1985.tb09138.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:551 / 556
页数:6
相关论文
共 23 条
[1]  
BASNER R, 1979, J BIOL CHEM, V245, P1151
[2]   DYGGVE-MELCHIOR-CLAUSEN SYNDROME - NORMAL DEGRADATION OF PROTEODERMATAN SULFATE, PROTEOKERATAN SULFATE AND HEPARAN-SULFATE [J].
BECK, M ;
LUCKE, R ;
KRESSE, H .
CLINICA CHIMICA ACTA, 1984, 141 (01) :7-15
[3]   A MODIFIED URONIC ACID CARBAZOLE REACTION [J].
BITTER, T ;
MUIR, HM .
ANALYTICAL BIOCHEMISTRY, 1962, 4 (04) :330-&
[4]  
BOAS NF, 1953, J BIOL CHEM, V204, P553
[5]   REGULATION OF PROSTAGLANDIN SYNTHESIS AND OF SELECTIVE RELEASE OF LYSOSOMAL HYDROLASES BY MOUSE PERITONEAL MACROPHAGES [J].
BONNEY, RJ ;
WIGHTMAN, PD ;
DAVIES, P ;
SADOWSKI, SJ ;
KUEHL, FA ;
HUMES, JL .
BIOCHEMICAL JOURNAL, 1978, 176 (02) :433-442
[6]   STRUCTURE OF KERATAN SULFATES FROM VARIOUS SOURCES [J].
CHOI, HU ;
MEYER, K .
BIOCHEMICAL JOURNAL, 1975, 151 (03) :543-553
[8]   SANFILIPPO TYPE-D DISEASE - CLINICAL FINDINGS IN 2 PATIENTS WITH A NEW VARIANT OF MUCOPOLYSACCHARIDOSIS-III [J].
GATTI, R ;
BORRONE, C ;
DEVIRGILIS, S ;
SANNA, G ;
CAO, A ;
VONFIGURA, K ;
KRESSE, H ;
PASCHKE, E ;
DURAND, P .
EUROPEAN JOURNAL OF PEDIATRICS, 1982, 138 (02) :168-171
[9]   IMPAIRED DEGRADATION OF KERATAN SULFATE BY MORQUIO-A FIBROBLASTS [J].
GLOSSL, J ;
KRESSE, H .
BIOCHEMICAL JOURNAL, 1982, 203 (01) :335-338
[10]  
GLOSSL J, 1983, BIOCHEM J, V215, P295