HETEROGENEITY IN THE MOLECULAR-BASIS OF 3 TYPES OF HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN AND THE RELATIVE SYNTHESIS OF THE G-GAMMA-TYPE AND A-GAMMA-TYPE OF GAMMA-CHAIN

被引:66
作者
KUTLAR, A
GARDINER, MB
HEADLEE, MG
REESE, AL
CLEEK, MP
NAGLE, S
SUKUMARAN, PK
HUISMAN, IHJ
机构
[1] MED COLL GEORGIA,DEPT CELL & MOLEC BIOL,CTR COMPREHENS SICKLE CELL,AUGUSTA,GA 30912
[2] MED COLL GEORGIA,DEPT CELL & MOLEC BIOL,PROT CHEM LAB,AUGUSTA,GA 30912
[3] VET ADM MED CTR,MED RES SERV,AUGUSTA,GA 30910
关键词
D O I
10.1007/BF00499284
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:21 / 35
页数:15
相关论文
共 26 条
  • [1] ABRAHAM E C, 1976, Hemoglobin, V1, P27, DOI 10.3109/03630267609031020
  • [2] BERNARDS R, 1980, NUCLEIC ACIDS RES, V8, P1521, DOI 10.1093/nar/8.7.1521
  • [3] ESTIMATION OF SMALL PERCENTAGES OF FOETAL HAEMOGLOBIN
    BETKE, K
    MARTI, HR
    SCHLICHT, I
    [J]. NATURE, 1959, 184 (4702) : 1877 - 1878
  • [4] NEGRO VARIETY OF HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN IS A MILD FORM OF THALASSEMIA
    CHARACHE, S
    CLEGG, JB
    WEATHERALL, DJ
    [J]. BRITISH JOURNAL OF HAEMATOLOGY, 1976, 34 (04) : 527 - 534
  • [5] GAMMA-CHAIN HETEROGENEITY OF FETAL HEMOGLOBIN IN NON-BLACK BETA-THALASSEMIA AND DELTA-BETA-THALASSEMIA AND HPFH HETEROZYGOTES AND HOMOZYGOTES
    EFREMOV, GD
    IBARRA, B
    GURGEY, A
    SUKUMARAN, PK
    ALTAY, C
    HUISMAN, THJ
    [J]. AMERICAN JOURNAL OF HEMATOLOGY, 1982, 12 (04) : 367 - 382
  • [6] THE DISTRIBUTION OF FETAL HEMOGLOBIN AND THE TYPES OF GAMMA-CHAIN IN RED-CELL FRACTIONS SEPARATED BY GRADIENT CENTRIFUGATION FROM BLOOD OF PATIENTS WITH SICKLE-CELL-ANEMIA AND OTHER HEMOGLOBINOPATHIES
    HEADLEE, ME
    GARDINER, MB
    REESE, AL
    HUISMAN, THJ
    [J]. BIOCHEMICAL MEDICINE, 1983, 29 (03): : 337 - 354
  • [7] HUISMAN THJ, 1981, BLOOD, V57, P75
  • [8] HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN - HETEROGENEITY OF FETAL HEMOGLOBIN IN HOMOZYGOTES AND IN CONJUNCTION WITH BETA-THALASSEMIA
    HUISMAN, THJ
    SHELTON, JB
    SCHROEDER, WA
    CHARACHE, S
    BETHLENFALVAY, NC
    BOUVER, N
    SHELTON, JR
    APELL, G
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1971, 285 (13) : 711 - +
  • [9] EVIDENCE FOR MULTIPLE STRUCTURAL GENES FOR GAMMA-CHAIN OF HUMAN FETAL HEMOGLOBIN IN HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN
    HUISMAN, THJ
    SCHROEDER, WA
    DOZY, AM
    SHELTON, JR
    SHELTON, JB
    BOYD, EM
    APELL, G
    [J]. ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1969, 165 (A1) : 320 - +
  • [10] PRESENT STATUS OF HETEOGENEITY OF FETAL HEMOGLOBIN IN BETA-THALASSEMIA - ATTEMPT TO UNIFY SOME OBSERVATIONS IN THALASSEMIA AND RELATED CONDITIONS
    HUISMAN, THJ
    SCHROEDER, WA
    EFREMOV, GD
    DUMA, H
    MLADENOVSKI, B
    HYMAN, CB
    RACHMILEWITZ, EA
    BOUVER, N
    MILLER, A
    BRODIE, A
    SHELTON, JR
    SHELTON, JB
    APELL, G
    [J]. ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1974, 232 (MAY24) : 107 - 124