STUDIES OF METHYLMALONYL-COENZYME A CARBONYLMUTASE ACTIVITY IN METHYLMALONIC ACIDEMIA .2. INVITRO BINDING KINETICS WITH ADENOSYLCOBALAMIN

被引：12

作者：

MORROW, G ^{[1
]}

LEBOWITZ, J ^{[1
]}

机构：

[1] UNIV ARIZONA,COLL MED,DEPT PEDIAT,TUCSON,AZ 85724

来源：

BIOCHEMICAL MEDICINE | 1976年 / 15卷 / 03期

关键词：

D O I：

10.1016/0006-2944(76)90054-5

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：241 / 245

页数：5

共 10 条

[1]

BARKER HA, 1961, FED PROC, V20, P956

[2]

CANNATA JJB, 1965, J BIOL CHEM, V240, P3249

[3] GENETIC COMPLEMENTATION IN HETEROKARYONS OF HUMAN FIBROBLASTS DEFECTIVE IN COBALAMIN METABOLISM [J].

GRAVEL, RA ;

MAHONEY, MJ ;

RUDDLE, FH ;

ROSENBERG, LE .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (08) :3181-3185

[4] INVITRO RESPONSIVE METHYLMALONIC ACIDEMIA - NEW VARIANT [J].

KAYE, CI ;

MORROW, G ;

NADLER, HL .

JOURNAL OF PEDIATRICS, 1974, 85 (01) :55-59

[5]

LOWRY OH, 1951, J BIOL CHEM, V193, P265

[6] METHYLMALONICACIDEMIA - BIOCHEMICAL HETEROGENEITY IN DEFECTS OF 5'-DEOXYADENOSYLCOBALAMIN SYNTHESIS [J].

MAHONEY, MJ ;

HART, AC ;

STEEN, VD ;

ROSENBERG, LE .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (07) :2799-2803

[7] CONGENITAL METHYLMALONIC ACIDEMIA - ENZYMATIC EVIDENCE FOR 2 FORMS OF DISEASE [J].

MORROW, G ;

BARNESS, LA ;

CARDINALE, GJ ;

ABELES, RH ;

FLAKS, JG .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 63 (01) :191-+

[8] STUDIES OF METHYLMALONYL COENZYME-A CARBONYLMUTASE ACTIVITY IN METHYLMALONIC ACIDEMIA .1. CORRELATION OF CLINICAL HEPATIC, AND FIBROBLAST DATA [J].

MORROW, G ;

MAHONEY, MJ ;

MATHEWS, C ;

LEBOWITZ, J .

PEDIATRIC RESEARCH, 1975, 9 (08) :641-644

[9] METHYLMALONIC ACIDURIA - AN INBORN ERROR OF METABOLISM LEADING TO CHRONIC METABOLIC ACIDOSIS [J].

OBERHOLZ.VG ;

LEVIN, B ;

BURGESS, EA ;

YOUNG, WF .

ARCHIVES OF DISEASE IN CHILDHOOD, 1967, 42 (225) :492-&

[10] METHYLMALONIC ACIDURIA - METABOLIC BLOCK LOCALIZATION AND VITAMIN B12 DEPENDENCY [J].

ROSENBERG, LE ;

LILLJEQVIST, AC ;

HSIA, YE .

SCIENCE, 1968, 162 (3855) :805-+

← 1 →