PROTEIN-DEGRADATION IN CULTURED SKELETAL-MUSCLE FROM DUCHENNE MUSCULAR-DYSTROPHY PATIENTS

被引:5
作者
NEVILLE, HE [1 ]
HARROLD, S [1 ]
机构
[1] UNIV COLORADO,SCH MED,DEPT NEUROL,NEUROMUSCULAR SECT,DENVER,CO 80202
关键词
D O I
10.1002/mus.880080312
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:253 / 257
页数:5
相关论文
共 25 条
[1]   INCREASED TURNOVER OF MUSCLE CONTRACTILE PROTEINS IN DUCHENNE MUSCULAR-DYSTROPHY AS ASSESSED BY 3-METHYLHISTIDINE AND CREATININE EXCRETION [J].
BALLARD, FJ ;
TOMAS, FM ;
STERN, LM .
CLINICAL SCIENCE, 1979, 56 (04) :347-352
[2]   DEFECTIVE MYOBLASTS IDENTIFIED IN DUCHENNE MUSCULAR-DYSTROPHY [J].
BLAU, HM ;
WEBSTER, C ;
PAVLATH, GK .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (15) :4856-4860
[3]   DECREASE IN THE RATE OF PROTEIN-SYNTHESIS BY POLYSOMES FROM CULTURED FIBROBLASTS OF PATIENTS AND CARRIERS WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
BOULE, M ;
VANASSE, M ;
BRAKIERGINGRAS, L .
CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES, 1979, 6 (03) :355-358
[4]  
Dubowitz V, 1973, MUSCLE BIOPSY MODERN, P5
[5]  
ETTIENNE EM, 1980, J BIOL CHEM, V256, P6408
[6]  
GARBER AJ, 1980, J BIOL CHEM, V255, P8315
[7]   MUSCLE WASTING IN MUSCULAR-DYSTROPHY - DECREASED PROTEIN-SYNTHESIS OR INCREASED DEGRADATION [J].
GRIGGS, RC ;
RENNIE, MJ .
ANNALS OF NEUROLOGY, 1983, 13 (02) :125-132
[8]   MYOGENESIS OF NORMAL AND DYSTROPHIC CHICK EMBRYONIC SKELETAL-MUSCLE CELLS INVITRO - BIOSYNTHESIS OF PLASMA-MEMBRANE PROTEINS [J].
HOLLAND, PC ;
CATES, GA ;
WENGER, BS ;
RANEY, BL .
CANADIAN JOURNAL OF BIOCHEMISTRY, 1980, 58 (10) :1156-1164
[9]   STIMULATORY EFFECTS OF DRUGS FOR PROTEIN-SYNTHESIS ON MUSCLE-CELL CULTURES IN DUCHENNE DYSTROPHY [J].
IONASESCU, V ;
STERN, LZ ;
IONASESCU, R ;
RUBENSTEIN, P .
ANNALS OF NEUROLOGY, 1979, 5 (02) :107-110
[10]   ALTERED PROTEIN-SYNTHESIS AND CREATINE-KINASE IN BREAST MUSCLE-CELL CULTURES FROM DYSTROPHIC CHICK-EMBRYOS - CORRECTIVE INFLUENCE OF LEUPEPTIN, PEPSTATIN AND DIPHENYLHYDANTOIN [J].
IONASESCU, V ;
IONASESCU, R ;
WITTE, D ;
FELD, R ;
CANCILLA, P ;
KAEDING, L ;
KRAUS, L ;
STERN, L .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1980, 46 (02) :157-168