DAYTIME SLEEP IN MYOTONIC-DYSTROPHY IS NOT CAUSED BY SLEEP-APNEA

被引:65
作者
VANDERMECHE, FGA [1 ]
BOGAARD, JM [1 ]
VANDERSLUYS, JCM [1 ]
SCHIMSHEIMER, RJ [1 ]
VERVERS, CCM [1 ]
BUSCH, HFM [1 ]
机构
[1] UNIV HOSP DIJKZIGT,DEPT PULM DIS,ROTTERDAM,NETHERLANDS
关键词
D O I
10.1136/jnnp.57.5.626
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Daytime sleepiness is common in myotonic dystrophy and might be attributed to disturbed nocturnal breathing. Seventeen out of 22 patients complained of excessive daytime sleepiness, resembling ''idiopathic hypersomnolence'' Sleep apnoea might have contributed to daytime sleepiness in only three of 17 patients. Treatment with the central stimulant methylphenidate produced sustained benefit in seven out of 11 patients tested. Daytime sleepiness in myotonic dystrophy is usually caused by dysfunction of central sleep regulation and not by disturbed nocturnal breathing.
引用
收藏
页码:626 / 628
页数:3
相关论文
共 9 条
[1]   SLEEP-RELATED BREATHING IMPAIRMENT IN MYOTONIC-DYSTROPHY [J].
CIRIGNOTTA, F ;
MONDINI, S ;
ZUCCONI, M ;
BARROTCORTES, E ;
STURANI, C ;
SCHIAVINA, M ;
COCCAGNA, G ;
LUGARESI, E .
JOURNAL OF NEUROLOGY, 1987, 235 (02) :80-85
[2]  
CUMMISKEY J, 1978, SLEEP APNEA SYNDROME, P295
[3]   PHRENIC NERVE CONDUCTION IN MAN [J].
DAVIS, JN .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1967, 30 (05) :420-&
[4]   SNORING .1. DAYTIME SLEEPINESS IN REGULAR HEAVY SNORERS [J].
GUILLEMINAULT, C ;
STOOHS, R ;
DUNCAN, S .
CHEST, 1991, 99 (01) :40-48
[5]   CARDIOPULMONARY INSUFFICIENCY IN MYOTONIC AND PROGRESSIVE MUSCULAR DYSTROPHY [J].
KILBURN, KH ;
EAGAN, JT ;
SIEKER, HO ;
HEYMAN, A .
NEW ENGLAND JOURNAL OF MEDICINE, 1959, 261 (22) :1089-1096
[6]  
Myotonic Dystrophy Foundation, 2017, VOIC PAT REP MYOT DY
[7]  
Parkes JD., 1985, SLEEP ITS DISORDERS
[8]  
Rechtschaffen Allan, 1968, MANUAL STANDARDIZED
[9]   TREATMENT OF HYPERSOMNOLENCE IN MYOTONIC-DYSTROPHY WITH A CNS STIMULANT [J].
VANDERMECHE, FGA ;
BOOGAARD, JM ;
VANDENBERG, B .
MUSCLE & NERVE, 1986, 9 (04) :341-344