METACHROMATIC FORM OF DIFFUSE CEREBRAL SCLEROSIS .V. NATURE AND SIGNIFICANCE OF LOW SULFATASE ACTIVITY - A CONTROLLED STUDY OF BRAIN LIVER AND KIDNEY IN 4 PATIENTS WITH METACHROMATIC LEUKODYSTROPHY (MLD)

被引:186
作者
AUSTIN, J
ARMSTRONG, D
SHEARER, L
机构
关键词
D O I
10.1001/archneur.1965.00470060029003
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:593 / +
页数:1
相关论文
共 79 条
[1]  
ARMSTRONG DR, TO BE PUBLISHED
[2]   ELECTRON MICROSCOPIC OBSERVATIONS ON METACHROMATIC LEUKODYSTROPHY [J].
AUREBECK, G ;
NELSON, E ;
CHOU, S ;
BLAW, M ;
OSTERBERG, KA .
ARCHIVES OF NEUROLOGY, 1964, 11 (03) :273-&
[3]   METACHROMATIC FORM OF DIFFUSE CEREBRAL SCLEROSIS .4. LOW SULFATASE ACTIVITY IN URINE OF NINE LIVING PATIENTS WITH METACHROMATIC LEUKODYSTROPHY (MLD) [J].
AUSTIN, J ;
MCAFEE, D ;
SHEARER, L .
ARCHIVES OF NEUROLOGY, 1965, 12 (05) :447-&
[4]   ABNORMAL SULPHATASE ACTIVITIES IN 2 HUMAN DISEASES ( METACHROMATIC LEUCODYSTROPHY + GARGOYLISM ) [J].
AUSTIN, J ;
SHEARER, L ;
ARMSTRONG, D ;
MCAFEE, D ;
OROURKE, M ;
BACHHAWAT, B .
BIOCHEMICAL JOURNAL, 1964, 93 (02) :C15-&
[5]  
AUSTIN J, TO BE PUBLISHED
[6]  
AUSTIN J, 1965, MEDICAL ASPECTS MENT, P813
[7]  
AUSTIN JAMES, 1964, TRANS AMER NEUROL ASS, V89, P147
[9]   A CONTROLLED STUDY OF ENZYMIC ACTIVITIES IN 3 HUMAN DISORDERS OF GLYCOLIPID METABOLISM [J].
AUSTIN, JH ;
BALASUBRAMANIAN, AS ;
BACHHAWAT, BK ;
BASU, DK ;
SARASWATHI, S ;
PATTABIRAMAN, TN .
JOURNAL OF NEUROCHEMISTRY, 1963, 10 (11) :805-&
[10]   A HISTOCHEMICAL METHOD FOR SULFATASE ACTIVITY IN HEMIC CELLS AND ORGAN IMPRINTS [J].
AUSTIN, JH ;
BISCHEL, M .
BLOOD, 1961, 17 (02) :216-&