HEMOGLOBIN BETH ISRAEL - MUTANT CAUSING CLINICALLY APPARENT CYANOSIS

被引:50
作者
NAGEL, RL
LYNFIELD, J
JOHNSON, J
LANDAU, L
BOOKCHIN, RM
HARRIS, MB
机构
[1] YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT MED,DIV HEMATOL,BRONX,NY 10461
[2] NYU BETH ISRAEL MED CTR,DEPT PEDIAT,NEW YORK,NY
关键词
D O I
10.1056/NEJM197607152950302
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:125 / 130
页数:6
相关论文
共 28 条
[1]   ERYTHROCYTOSIS ASSOCIATED WITH HEMOGLOBIN RAINIER - OXYGEN EQUILIBRIA AND MARROW REGULATION [J].
ADAMSON, JW ;
PARER, JT ;
STAMATOYANNOPOULOS, G ;
HEINENBE.S .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (08) :1376-+
[2]  
ALLEN DW, 1950, J BIOL CHEM, V187, P393
[3]   STRUCTURES OF DEOXY AND CARBONMONOXY HEMOGLOBIN KANSAS IN DEOXY QUATERNARY CONFORMATION [J].
ANDERSON, L .
JOURNAL OF MOLECULAR BIOLOGY, 1975, 94 (01) :33-&
[4]   Protein coagulation and its reversal - The preparation of insoluble globin, soluble globin and heme [J].
Anson, ML ;
Mirsky, AE .
JOURNAL OF GENERAL PHYSIOLOGY, 1930, 13 (04) :469-476
[5]  
ANTONINI E, 1971, HEMOGLOBIN MYOGLOBIN, V21
[6]  
BONAVENTURA J, 1968, J BIOL CHEM, V243, P980
[7]  
BOOKCHIN RM, 1967, J BIOL CHEM, V242, P248
[8]  
BUCCI E, 1965, J BIOL CHEM, V240, P551
[9]   ABNORMAL HUMAN HAEMOGLOBINS - SEPARATION AND CHARACTERIZATION OF ALPHA AND BETA CHAINS BY CHROMATOGRAPHY AND DETERMINATION OF 2 NEW VARIANTS HB CHESAPEAKE AND HB J (BANGKOK) [J].
CLEGG, JB ;
NAUGHTON, MA ;
WEATHERA.DJ .
JOURNAL OF MOLECULAR BIOLOGY, 1966, 19 (01) :91-&
[10]  
Dacie J.V., 1991, PRACTICAL HAEMATOLOG, P54