I-CELL DISEASE (MUCOLIPIDOSIS II) - RESOLUTION OF N-ACETYL-BETA-D-GLUCOSAMINIDASE AND ALPHA-L-FUCOSIDASE COMPONENTS BY DEAE-CELLULOSE CHROMATOGRAPHY

被引：13

作者：

ELLIS, RB

WILLCOX, P

PATRICK, AD

机构：

[1] INST CHILD HLTH,DEPT CHEM PATHOL,30 GUILFORD ST,LONDON WC1N 1EH,ENGLAND

[2] INST CHILD HLTH,MRC,CLIN GENET UNIT,30 GUILFORD ST,LONDON WC1N 1EH,ENGLAND

来源：

CLINICAL SCIENCE AND MOLECULAR MEDICINE | 1975年 / 49卷 / 06期

关键词：

D O I：

10.1042/cs0490543

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：543 / 550

页数：8

共 18 条

[1]

BARTHOLOMEW BA, 1973, J BIOL CHEM, V248, P5751

[2]

CARLSON DM, 1973, J BIOL CHEM, V248, P5742

[3]

DENTANDT WR, 1974, J LAB CLIN MED, V83, P403

[4] SUBSTRATE-SPECIFICITY OF NEURAMINIDASES [J].

DRZENIEK, R .

HISTOCHEMICAL JOURNAL, 1973, 5 (03) :271-290

[5] DEAE-CELLULOSE MICROCOLUMN CHROMATOGRAPHY COUPLED WITH AUTOMATED ASSAY - APPLICATION TO RESOLUTION OF N-ACETYL-BETA-D-HEXOSAMINIDASE COMPONENTS [J].

ELLIS, RB ;

IKONNE, JU ;

MASSON, PK .

ANALYTICAL BIOCHEMISTRY, 1975, 63 (01) :5-11

[6] PHYSICOCHEMICAL MODIFICATIONS OF LYSOSOMAL HYDROLASES DURING INTRACELLULAR TRANSPORT [J].

GOLDSTONE, A ;

KOENIG, H .

BIOCHEMICAL JOURNAL, 1973, 132 (02) :267-+

[7]

GOTTSCHALK A, 1972, GLYCOPROTEINS THEIR, V5

[8] HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES [J].

HICKMAN, S ;

NEUFELD, EF .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 49 (04) :992-&

[9] EVIDENCE FOR 2 CMP-N-ACETYLNEURAMINIC ACID - LACTOSE SIALYLTRANSFERASES IN RAT, PORCINE, BOVINE, AND HUMAN LIVER [J].

HUDGIN, RL ;

SCHACHTER, H .

CANADIAN JOURNAL OF BIOCHEMISTRY, 1972, 50 (09) :1024-+

[10] N-ACETYL-BETA-D-HEXOSAMINIDASE COMPONENT-A - DIFFERENT FORMS IN HUMAN TISSUES AND FLUIDS [J].

IKONNE, JU ;

ELLIS, RB .

BIOCHEMICAL JOURNAL, 1973, 135 (03) :457-462

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