ANGIOMYOLIPOMAS OF THE LIVER IN TUBEROUS SCLEROSIS

被引:35
作者
CARMODY, E
YEUNG, E
MCLOUGHLIN, M
机构
[1] General Division, Department of Diagnostic Radiology, The Toronto Hospital, Toronto, M5G 2C4, Ontario
来源
ABDOMINAL IMAGING | 1994年 / 19卷 / 06期
关键词
TUBEROUS SCLEROSIS; HEPATIC ANGIOMYOLIPOMAS;
D O I
10.1007/BF00198257
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Although the association of tuberous sclerosis and renal angiomyolipomas is well established, the occurrence of hepatic hamartomatous lesions in this disease is less well documented. We describe two cases of tuberous sclerosis with associated multiple intrahepatic angiomyolipomas, and we review the literature on this subject. Radiologically, angiomyolipomas can range from entirely lipomatous to completely solid, features which are present in our cases. A characteristic finding of the hepatic involvement in this disease appears to be the multiplicity of the lesions. We suggest that in the setting of tuberous sclerosis it is reasonable to assume that intrahepatic lesions represent angiomyolipomas. However, in nontuberous sclerosis patients with similar findings malignancy cannot be excluded.
引用
收藏
页码:537 / 539
页数:3
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