RENAL TUBULAR DYSGENESIS WITHOUT PULMONARY HYPOPLASIA

被引：11

作者：

SCARCELLA, A

PECORARO, C

DAGNELLO, MR

SOLE, AN

机构：

[1] Department of Paediatrics, University Federico II, Naples

来源：

PEDIATRIC NEPHROLOGY | 1994年 / 8卷 / 02期

关键词：

POTTER SEQUENCE; RENAL TUBULAR DYSGENESIS; OLIGOHYDRAMNIOS; PULMONARY HYPOPLASIA; RENAL FAILURE;

D O I：

10.1007/BF00865484

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Only a few cases of renal tubular dysgenesis (RTD) have been diagnosed. RTD is associated with a very early death, always due to lethal pulmonary hypoplasia. We report an additional patient, interesting for two reasons: (1) the rarity of RTD, (2) the absence of microscopic and macroscopic anatomical alterations of the lungs. The infant had only a mild, transient pulmonary maladaptation; after a few days of life the pulmonary function returned to normal. Although renal function dramatically improved after institution of peritoneal dialysis at 6 days of life, the patient died after 2 weeks with an overwhelming Candida sepsis. We suggest that the lack of pulmonary hypoplasia might be due to a short exposure to oligohydramnios.

引用

页码：216 / 217

页数：2

共 12 条

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