SUCCESSFUL REPAIR INUTERO OF A FETAL DIAPHRAGMATIC-HERNIA AFTER REMOVAL OF HERNIATED VISCERA FROM THE LEFT THORAX

被引:212
作者
HARRISON, MR
ADZICK, NS
LONGAKER, MT
GOLDBERG, JD
ROSEN, MA
FILLY, RA
EVANS, MI
GOLBUS, MS
机构
[1] UNIV CALIF SAN FRANCISCO, FETAL TREATMENT PROGRAM, SAN FRANCISCO, CA 94143 USA
[2] UNIV CALIF SAN FRANCISCO, DEPT OBSTET GYNECOL & REPROD SCI, SAN FRANCISCO, CA 94143 USA
[3] UNIV CALIF SAN FRANCISCO, DEPT RADIOL, SAN FRANCISCO, CA 94143 USA
[4] UNIV CALIF SAN FRANCISCO, DEPT ANESTHESIA, SAN FRANCISCO, CA 94143 USA
[5] WAYNE STATE UNIV, DEPT OBSTET & GYNECOL, DETROIT, MI 48202 USA
关键词
D O I
10.1056/NEJM199005313222207
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
MOST infants with congenital diaphragmatic hernia die because their lungs are inadequate to support extrauterine life. This remains true despite advances in postnatal care, including preoperative stabilization,1,2 pharmacologic treatment of persistent pulmonary hypertension of the newborn,3,4 and temporary support with extracorporeal membrane oxygenation.5,6 Recently, prenatal diagnosis has allowed us to define the natural history of fetal diaphragmatic hernia better: approximately 75 percent of fetuses with congenital diaphragmatic hernia detected before birth die despite optimal postnatal care.7 8 9 10 11 The neonatal outcome is related to the degree of pulmonary hypoplasia from in utero lung compression, which is determined by the timing and volume.  . . © 1990, Massachusetts Medical Society. All rights reserved.
引用
收藏
页码:1582 / 1584
页数:3
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共 19 条
  • [1] CORRECTION OF CONGENITAL DIAPHRAGMATIC-HERNIA INUTERO .4. AN EARLY GESTATIONAL FETAL LAMB MODEL FOR PULMONARY VASCULAR MORPHOMETRIC ANALYSIS
    ADZICK, NS
    OUTWATER, KM
    HARRISON, MR
    DAVIES, P
    GLICK, PL
    DELORIMIER, AA
    REID, LM
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1985, 20 (06) : 673 - 680
  • [2] FETAL DIAPHRAGMATIC-HERNIA - ULTRASOUND DIAGNOSIS AND CLINICAL OUTCOME IN 38 CASES
    ADZICK, NS
    VACANTI, JP
    LILLEHEI, CW
    OROURKE, PP
    CRONE, RK
    WILSON, JM
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1989, 24 (07) : 654 - 658
  • [3] FETAL SURGERY IN THE PRIMATE .3. MATERNAL OUTCOME AFTER FETAL SURGERY
    ADZICK, NS
    HARRISON, MR
    GLICK, PL
    ANDERSON, J
    VILLA, RL
    FLAKE, AW
    LABERGE, JM
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1986, 21 (06) : 477 - 480
  • [4] DIAPHRAGMATIC-HERNIA IN THE FETUS - PRENATAL-DIAGNOSIS AND OUTCOME IN 94 CASES
    ADZICK, NS
    HARRISON, MR
    GLICK, PL
    NAKAYAMA, DK
    MANNING, FA
    DELORIMIER, AA
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1985, 20 (04) : 357 - 361
  • [5] EXTRACORPOREAL MEMBRANE-OXYGENATION (ECMO) IN NEONATAL RESPIRATORY-FAILURE - 100 CASES
    BARTLETT, RH
    GAZZANIGA, AB
    TOOMASIAN, J
    CORWIN, AG
    ROLOFF, D
    RUCKER, R
    [J]. ANNALS OF SURGERY, 1986, 204 (03) : 236 - 245
  • [6] FETAL DIAPHRAGMATIC-HERNIA - ULTRASOUND DIAGNOSIS AND CLINICAL OUTCOME IN 19 CASES
    BENACERRAF, BR
    ADZICK, NS
    [J]. AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY, 1987, 156 (03) : 573 - 576
  • [7] VENTILATORY PREDICTORS OF PULMONARY HYPOPLASIA IN CONGENITAL DIAPHRAGMATIC-HERNIA, CONFIRMED BY MORPHOLOGICAL ASSESSMENT
    BOHN, D
    TAMURA, M
    PERRIN, D
    BARKER, G
    RABINOVITCH, M
    [J]. JOURNAL OF PEDIATRICS, 1987, 111 (03) : 423 - 431
  • [8] CONGENITAL DIAPHRAGMATIC-HERNIA - ARTERIAL STRUCTURAL-CHANGES AND PERSISTENT PULMONARY-HYPERTENSION AFTER SURGICAL REPAIR
    GEGGEL, RL
    MURPHY, JD
    LANGLEBEN, D
    CRONE, RK
    VACANTI, JP
    REID, LM
    [J]. JOURNAL OF PEDIATRICS, 1985, 107 (03) : 457 - 464
  • [9] CORRECTION OF CONGENITAL DIAPHRAGMATIC-HERNIA IN UTERO, .5. INITIAL CLINICAL-EXPERIENCE
    HARRISON, MR
    LANGER, JC
    ADZICK, NS
    GOLBUS, MS
    FILLY, RA
    ANDERSON, RL
    ROSEN, MA
    CALLEN, PW
    GOLDSTEIN, RB
    DELORIMIER, AA
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1990, 25 (01) : 47 - 57
  • [10] FETAL SURGERY IN THE PRIMATE .1. ANESTHETIC, SURGICAL, AND TOCOLYTIC MANAGEMENT TO MAXIMIZE FETAL-NEONATAL SURVIVAL
    HARRISON, MR
    ANDERSON, J
    ROSEN, MA
    ROSS, NA
    HENDRICKX, AG
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1982, 17 (02) : 115 - 122