PRIMARY CENTRAL-NERVOUS-SYSTEM INVOLVEMENT OF THE SO-CALLED PERIPHERAL T-CELL LYMPHOMA - REPORT OF A CASE AND REVIEW OF THE LITERATURE

被引:12
作者
MINEURA, K [1 ]
SAWATAISHI, J [1 ]
SASAJIMA, T [1 ]
KOWADA, M [1 ]
SUGAWARA, A [1 ]
EBINA, K [1 ]
机构
[1] NAKADORI HOSP,DEPT NEUROSURG,AKITA,AKITA,JAPAN
关键词
CENTRAL NERVOUS SYSTEM; LYMPHOMA; T-CELL;
D O I
10.1007/BF01057040
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Primary central nervous system (CNS) involvement of non-Hodgkin's lymphoma is uncommon and a vast majority of reported cases are of B-cell origin. We present a 52-year-old woman with primary peripheral T-cell lymphoma of the brain. Immunostaining of paraffin-embedded sections proved tumor cells to be positive for T-cell markers MT1 and UCHL1, and negative for B-cell markers MB1, and 4KB5. Radiotherapy combined with steroid therapy rendered neurologic recovery and complete tumor remission confirmed by computed tomography and magnetic resonance imaging. From a review of documented 19 cases of primary CNS T-cell lymphoma including the present case, this disease is characterized by poor prognosis among CNS lymphomas.
引用
收藏
页码:235 / 242
页数:8
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