PROLONGED QT, ATRIOVENTRICULAR-BLOCK, AND SUDDEN-DEATH IN THE NEWBORN - AN ELECTROPHYSIOLOGIC EVALUATION

被引:17
作者
SAOUDI, N [1 ]
BOZIO, A [1 ]
KIRKORIAN, G [1 ]
ATALLAH, G [1 ]
NORMAND, J [1 ]
TOUBOUL, P [1 ]
机构
[1] HOP CARDIOL,LYONS,FRANCE
关键词
2/1 ATRIOVENTRICULAR BLOCK; INFRAHISIAN BLOCK; CONGENITAL LONG QT SYNDROME;
D O I
10.1093/eurheartj/12.7.838
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
An electrophysiologic study was performed in the first month of life in a patient with the congenital long QT syndrome and spontaneous episodes of 2/1 atrioventricular block. The block could be reproduced by incremental atrial pacing, and its infrahisian location was associated with a prolongation of the refractoriness in the ventricular muscle itself. Surprisingly, intravenous propranolol aggravated this phenomenon by further prolonging the QT interval.Sudden death occurred shortly thereafter during Holter monitoring and was due to a sudden resumption of normal A V conduction after an episode of 2:1 block, immediately followed by ventricular fibrillation.
引用
收藏
页码:838 / 841
页数:4
相关论文
共 19 条
[1]  
BATISSE A, 1981, ARCH FR PEDIATR, V38, P657
[2]  
BATISSE A, 1987, TROUBLES RYTHME CARD, P15
[3]   TORSADE-DE-POINTES AND OTHER PAUSE-INDUCED VENTRICULAR TACHYCARDIAS - THE SHORT-LONG-SHORT SEQUENCE AND EARLY AFTERDEPOLARIZATIONS [J].
CRANEFIELD, PF ;
ARONSON, RS .
PACE-PACING AND CLINICAL ELECTROPHYSIOLOGY, 1988, 11 (06) :670-678
[4]  
CRANEFIELD PF, 1988, CARDIAC ARRHYTHMIAS, P553
[5]   PERMANENT CARDIAC PACING IN PATIENTS WITH THE LONG QT SYNDROME [J].
ELDAR, M ;
GRIFFIN, JC ;
ABBOTT, JA ;
BENDITT, D ;
BHANDARI, A ;
HERRE, JM ;
BENSON, DW ;
SCHEINMAN, MM .
JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1987, 10 (03) :600-607
[6]  
ELSHERIF N, 1988, J AM COLL CARDIOL, V2, pA254
[7]  
ESCHER E, 1983, PEDIAT CARDIOL, V4, P121
[8]   CONGENITAL COMPLETE HEART-BLOCK AND LONG Q-T SYNDROME REQUIRING VENTRICULAR PACING FOR CONTROL OF REFRACTORY VENTRICULAR TACHYCARDIA AND FIBRILLATION [J].
GASCHO, JA ;
SCHIEKEN, R .
JOURNAL OF ELECTROCARDIOLOGY, 1979, 12 (03) :331-335
[9]  
KERNOHAN RJ, 1974, BRIT HEART J, V36, P516
[10]   ELECTROPHYSIOLOGIC EFFECTS OF PROPRANOLOL IN INTRAVENTRICULAR-CONDUCTION DISTURBANCE [J].
KIRKORIAN, G ;
TOUBOUL, P ;
ATALLAH, G .
AMERICAN JOURNAL OF CARDIOLOGY, 1988, 61 (04) :341-345