INTRACELLULAR POLYMERIZATION OF SICKLE HEMOGLOBIN - EFFECTS OF CELL HETEROGENEITY

被引:101
作者
NOGUCHI, CT [1 ]
TORCHIA, DA [1 ]
SCHECHTER, AN [1 ]
机构
[1] NIDR,BIOCHEM LAB,BETHESDA,MD 20205
关键词
D O I
10.1172/JCI111055
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:846 / 852
页数:7
相关论文
共 31 条
  • [1] MINOR HEMOGLOBINS IN SICKLE-CELL ANEMIA, BETA-THALASSEMIA, AND RELATED CONDITIONS - STUDY OF RED-CELL FRACTIONS ISOLATED BY DENSITY GRADIENT CENTRIFUGATION
    ABRAHAM, EC
    WALKER, D
    GRAVELY, M
    HUISMAN, THJ
    [J]. BIOCHEMICAL MEDICINE, 1975, 13 (01): : 56 - 77
  • [2] BRITTENHAM GM, 1982, BLOOD S1, V60, pA43
  • [3] MOLECULAR AND CELLULAR PATHOGENESIS OF HEMOGLOBIN-SC DISEASE
    BUNN, HF
    NOGUCHI, CT
    HOFRICHTER, J
    SCHECHTER, GP
    SCHECHTER, AN
    EATON, WA
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (23): : 7527 - 7531
  • [4] CHIEN S, 1978, BLOOD CELLS, V3, P279
  • [5] CLARK MR, 1976, BLOOD, V48, P899
  • [6] CLARK MR, 1982, BLOOD, V60, P659
  • [7] DEFORMABILITY OF OXYGENATED IRREVERSIBLY SICKLED CELLS
    CLARK, MR
    MOHANDAS, N
    SHOHET, SB
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1980, 65 (01) : 189 - 196
  • [8] KINETICS OF SICKLE HEMOGLOBIN POLYMERIZATION IN SINGLE RED-CELLS
    COLETTA, M
    HOFRICHTER, J
    FERRONE, FA
    EATON, WA
    [J]. NATURE, 1982, 300 (5888) : 194 - 197
  • [9] CORASH LM, 1974, J LAB CLIN MED, V84, P147
  • [10] F-CELL PRODUCTION IN SICKLE-CELL-ANEMIA - REGULATION BY GENES LINKED TO BETA-HEMOGLOBIN LOCUS
    DOVER, GJ
    BOYER, SH
    PEMBREY, ME
    [J]. SCIENCE, 1981, 211 (4489) : 1441 - 1444