KINETICS OF THE ASSEMBLY OF PEROXISOMES AFTER FUSION OF COMPLEMENTARY CELL-LINES FROM PATIENTS WITH THE CEREBRO-HEPATO-RENAL (ZELLWEGER) SYNDROME AND RELATED DISORDERS

被引:40
作者
BRUL, S
WIEMER, EAC
WESTERVELD, A
STRIJLAND, A
WANDERS, RJA
SCHRAM, AW
HEYMANS, HSA
SCHUTGENS, RBH
VANDENBOSCH, H
TAGER, JM
机构
[1] UNIV AMSTERDAM,BIOCHEM LAB,1000 HD AMSTERDAM,NETHERLANDS
[2] ERASMUS UNIV,DIV CELL BIOL & GENET,3000 DR ROTTERDAM,NETHERLANDS
[3] UNIV AMSTERDAM HOSP,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
[4] STATE UNIV UTRECHT,BIOCHEM LAB,3584 CH UTRECHT,NETHERLANDS
关键词
D O I
10.1016/S0006-291X(88)80395-4
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1083 / 1089
页数:7
相关论文
共 27 条
[2]  
BREMER J, 1977, TRENDS BIOCHEM SCI, V2, P207
[3]  
BRUL S, 1988, IN PRESS J CLIN INVE
[4]   PEROXISOMAL ALANINE - GLYOXYLATE AMINOTRANSFERASE DEFICIENCY IN PRIMARY HYPEROXALURIA TYPE-I [J].
DANPURE, CJ ;
JENNINGS, PR .
FEBS LETTERS, 1986, 201 (01) :20-24
[5]   CHAIN-SHORTENING OF PROSTAGLANDIN-F2-ALPHA BY RAT-LIVER PEROXISOMES [J].
DICZFALUSY, U ;
ALEXSON, SEH ;
PEDERSEN, JI .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1987, 144 (03) :1206-1213
[6]   ISOLATION OF INTRACELLULAR MEMBRANES BY MEANS OF SODIUM-CARBONATE TREATMENT - APPLICATION TO ENDOPLASMIC-RETICULUM [J].
FUJIKI, Y ;
HUBBARD, AL ;
FOWLER, S ;
LAZAROW, PB .
JOURNAL OF CELL BIOLOGY, 1982, 93 (01) :97-102
[7]   PEROXISOMAL AND MITOCHONDRIAL DEFECTS IN CEREBRO-HEPATO-RENAL SYNDROME [J].
GOLDFISCHER, S ;
MOORE, CL ;
JOHNSON, AB ;
SPIRO, AJ ;
VALSAMIS, MP ;
WISNIEWSKI, HK ;
RITCH, RH ;
NORTON, WT ;
RAPIN, I ;
GARTNER, LM .
SCIENCE, 1973, 182 (4107) :62-64
[8]   PEROXISOMAL DEFECTS IN NEONATAL-ONSET AND X-LINKED ADRENOLEUKODYSTROPHIES [J].
GOLDFISCHER, S ;
COLLINS, J ;
RAPIN, I ;
COLTOFFSCHILLER, B ;
CHANG, CH ;
NIGRO, M ;
BLACK, VH ;
JAVITT, NB ;
MOSER, HW ;
LAZAROW, PB .
SCIENCE, 1985, 227 (4682) :67-70
[9]  
GOLDFISCHER S, 1984, INT REV EXP PATHOL, V26, P45
[10]   DEGRADATION OF CHOLESTEROL TO PROPIONIC-ACID BY RAT-LIVER PEROXISOMES [J].
HAGEY, LR ;
KRISANS, SK .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1982, 107 (03) :834-841