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MULTIPLE DEFECTS OF THE RESPIRATORY-CHAIN INCLUDING COMPLEX-II IN A FAMILY WITH MYOPATHY AND ENCEPHALOPATHY
被引:26
作者
:
DESNUELLE, C
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
DESNUELLE, C
BIRCHMACHIN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
BIRCHMACHIN, M
PELLISSIER, JF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
PELLISSIER, JF
BINDOFF, LA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
BINDOFF, LA
ACKRELL, BAC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
ACKRELL, BAC
TURNBULL, DM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
TURNBULL, DM
机构
:
[1]
UNIV NEWCASTLE,SCH MED,DEPT CLIN NEUROSCI,DIV CLIN NEUROSCI,FRAMLINGTON PL,NEWCASTLE TYNE NE2 4HH,ENGLAND
[2]
CHU TIMONE,MALAD SYST NERVEUX CLIN,F-13385 MARSEILLE 5,FRANCE
[3]
VET ADM MED CTR,SAN FRANCISCO,CA 94121
[4]
UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143
来源
:
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
|
1989年
/ 163卷
/ 02期
关键词
:
D O I
:
10.1016/0006-291X(89)92279-1
中图分类号
:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号
:
071010 ;
081704 ;
摘要
:
引用
收藏
页码:695 / 700
页数:6
相关论文
共 29 条
[1]
Ackrell B A, 1978, Methods Enzymol, V53, P466
[2]
ACKRELL BAC, 1980, J BIOL CHEM, V255, P2761
[3]
ACKRELL BAC, 1984, J BIOL CHEM, V259, P53
[4]
BAGINSKY ML, 1969, J BIOL CHEM, V244, P5313
[5]
MITOCHONDRIAL MYOPATHY WITH LACTIC-ACIDOSIS AND DEFICIENT ACTIVITY OF MUSCLE SUCCINATE CYTOCHROME-C-OXIDOREDUCTASE
BEHBEHANI, AW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BEHBEHANI, AW
GOEBEL, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
GOEBEL, H
OSSE, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
OSSE, G
GABRIEL, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
GABRIEL, M
LANGENBECK, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
LANGENBECK, U
BERDEN, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BERDEN, J
BERGER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BERGER, R
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
SCHUTGENS, RBH
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1984,
143
(01)
: 67
-
71
[6]
STUDIES ON SUCCINATE-DEHYDROGENASE .30. INTERRELATIONS OF RECONSTITUTION ACTIVITY, REACTIONS WITH ELECTRON-ACCEPTORS, AND IRON-SULFUR CENTERS IN SUCCINATE-DEHYDROGENASE
BEINERT, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
BEINERT, H
ACKRELL, BAC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
ACKRELL, BAC
VINOGRADOV, AD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
VINOGRADOV, AD
KEARNEY, EB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
KEARNEY, EB
SINGER, TP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
SINGER, TP
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1977,
182
(01)
: 95
-
106
[7]
FATAL LACTIC-ACIDOSIS IN INFANCY WITH A DEFECT OF COMPLEX-III OF THE RESPIRATORY-CHAIN
BIRCHMACHIN, MA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
BIRCHMACHIN, MA
SHEPHERD, IM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
SHEPHERD, IM
WATMOUGH, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
WATMOUGH, NJ
SHERRATT, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
SHERRATT, HSA
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
BARTLETT, K
DARLEYUSMAR, VM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
DARLEYUSMAR, VM
MILLIGAN, DWA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
MILLIGAN, DWA
WELCH, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
WELCH, RJ
AYNSLEYGREEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
AYNSLEYGREEN, A
TURNBULL, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
TURNBULL, DM
[J].
PEDIATRIC RESEARCH,
1989,
25
(05)
: 553
-
559
[8]
POLYPEPTIDES IN SUCCINATE-COENZYME-Q REDUCTASE SEGMENT OF RESPIRATORY-CHAIN .8.
CAPALDI, RA
论文数:
0
引用数:
0
h-index:
0
CAPALDI, RA
SWEETLAND, J
论文数:
0
引用数:
0
h-index:
0
SWEETLAND, J
MERLI, A
论文数:
0
引用数:
0
h-index:
0
MERLI, A
[J].
BIOCHEMISTRY,
1977,
16
(26)
: 5707
-
5710
[9]
CHOMYN A, 1988, J BIOL CHEM, V263, P16395
[10]
BIOSYNTHESIS AND PROCESSING OF THE LARGE AND SMALL SUBUNITS OF SUCCINATE-DEHYDROGENASE IN CULTURED-MAMMALIAN-CELLS
CLARKSON, GHD
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
CLARKSON, GHD
KING, TE
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
KING, TE
LINDSAY, JG
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
LINDSAY, JG
[J].
BIOCHEMICAL JOURNAL,
1987,
244
(01)
: 15
-
20
←
1
2
3
→
共 29 条
[1]
Ackrell B A, 1978, Methods Enzymol, V53, P466
[2]
ACKRELL BAC, 1980, J BIOL CHEM, V255, P2761
[3]
ACKRELL BAC, 1984, J BIOL CHEM, V259, P53
[4]
BAGINSKY ML, 1969, J BIOL CHEM, V244, P5313
[5]
MITOCHONDRIAL MYOPATHY WITH LACTIC-ACIDOSIS AND DEFICIENT ACTIVITY OF MUSCLE SUCCINATE CYTOCHROME-C-OXIDOREDUCTASE
BEHBEHANI, AW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BEHBEHANI, AW
GOEBEL, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
GOEBEL, H
OSSE, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
OSSE, G
GABRIEL, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
GABRIEL, M
LANGENBECK, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
LANGENBECK, U
BERDEN, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BERDEN, J
BERGER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
BERGER, R
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MAINZ,DEPT NEUROPATHOL,D-6500 MAINZ,FED REP GER
SCHUTGENS, RBH
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1984,
143
(01)
: 67
-
71
[6]
STUDIES ON SUCCINATE-DEHYDROGENASE .30. INTERRELATIONS OF RECONSTITUTION ACTIVITY, REACTIONS WITH ELECTRON-ACCEPTORS, AND IRON-SULFUR CENTERS IN SUCCINATE-DEHYDROGENASE
BEINERT, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
BEINERT, H
ACKRELL, BAC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
ACKRELL, BAC
VINOGRADOV, AD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
VINOGRADOV, AD
KEARNEY, EB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
KEARNEY, EB
SINGER, TP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WISCONSIN,INST ENZYME RES,MADISON,WI 53706
SINGER, TP
[J].
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS,
1977,
182
(01)
: 95
-
106
[7]
FATAL LACTIC-ACIDOSIS IN INFANCY WITH A DEFECT OF COMPLEX-III OF THE RESPIRATORY-CHAIN
BIRCHMACHIN, MA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
BIRCHMACHIN, MA
SHEPHERD, IM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
SHEPHERD, IM
WATMOUGH, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
WATMOUGH, NJ
SHERRATT, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
SHERRATT, HSA
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
BARTLETT, K
DARLEYUSMAR, VM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
DARLEYUSMAR, VM
MILLIGAN, DWA
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
MILLIGAN, DWA
WELCH, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
WELCH, RJ
AYNSLEYGREEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
AYNSLEYGREEN, A
TURNBULL, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WELLCOME RES LABS,BECKENHAM BR3 3BS,KENT,ENGLAND
TURNBULL, DM
[J].
PEDIATRIC RESEARCH,
1989,
25
(05)
: 553
-
559
[8]
POLYPEPTIDES IN SUCCINATE-COENZYME-Q REDUCTASE SEGMENT OF RESPIRATORY-CHAIN .8.
CAPALDI, RA
论文数:
0
引用数:
0
h-index:
0
CAPALDI, RA
SWEETLAND, J
论文数:
0
引用数:
0
h-index:
0
SWEETLAND, J
MERLI, A
论文数:
0
引用数:
0
h-index:
0
MERLI, A
[J].
BIOCHEMISTRY,
1977,
16
(26)
: 5707
-
5710
[9]
CHOMYN A, 1988, J BIOL CHEM, V263, P16395
[10]
BIOSYNTHESIS AND PROCESSING OF THE LARGE AND SMALL SUBUNITS OF SUCCINATE-DEHYDROGENASE IN CULTURED-MAMMALIAN-CELLS
CLARKSON, GHD
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
CLARKSON, GHD
KING, TE
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
KING, TE
LINDSAY, JG
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
SUNY ALBANY,DEPT CHEM,ALBANY,NY 12222
LINDSAY, JG
[J].
BIOCHEMICAL JOURNAL,
1987,
244
(01)
: 15
-
20
←
1
2
3
→